Literature DB >> 25964308

GFR in Patients with β-Thalassemia Major.

Gai Milo1, Revital Feige Gross Nevo1, Idit Pazgal2, Anat Gafter-Gvili2, Ofer Shpilberg2, Uzi Gafter3, Arie Erman2, Pinhas Stark2.   

Abstract

BACKGROUND AND OBJECTIVES: Patients with β-thalassemia major (TM) may have tubular dysfunction and glomerular dysfunction, primarily hyperfiltration, based on eGFR. Assessment of GFR based on serum creatinine concentration may overestimate GFR in these patients. This study sought to determine GFR by using inulin clearance and compare it with measured creatinine clearance (Ccr) and eGFR. DESIGN, SETTING, PARTICIPANTS & MEASUREMENTS: Patients followed up in an Israeli thalassemia clinic who had been regularly transfused for years and treated with deferasirox were included in the study. They were studied by inulin clearance, Ccr, the CKD Epidemiology Collaboration and the Modification of Diet in Renal Disease equations for eGFR, and the Cockcroft-Gault estimation for Ccr. Expected creatinine excretion rate and tubular creatinine secretion rate were calculated.
RESULTS: Nine white patients were studied. Results, given as medians, were as follows: serum creatinine was 0.59 mg/dl (below normal limits); GFR was low (76.6 ml/min per 1.73 m(2)) and reached the level of CKD; Ccr was 134.9 ml/min per 1.73 m(2), higher than the GFR because of a tubular creatinine secretion rate of 30.3 ml/min per 1.73 m(2) (this accounted for 40% of the Ccr); and eGFR calculated by the CKD Epidemiology Collaboration and Modification of Diet in Renal Disease equations and Cockcroft-Gault-estimated Ccr were 133, 141, and 168 ml/min per 1.73 m(2), respectively. These latter values were significantly higher than the GFR, reaching the hyperfiltration range, and indicated that the estimation techniques were clinically unacceptable as a method for measuring kidney function compared with the GFR according to Bland and Altman analyses.
CONCLUSIONS: Contrary to previous reports, patients in this study with TM had normal or reduced GFR. The estimating methods showed erroneous overestimation of GFR and were clinically unacceptable for GFR measurements in patients with TM by Bland and Altman analysis. Therefore, more accurate methods should be used for early detection of reduced GFR and prevention of its further decline toward CKD in these patients.
Copyright © 2015 by the American Society of Nephrology.

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Keywords:  chronic kidney disease; glomerular filtration rate; glomerular hyperfiltration

Mesh:

Substances:

Year:  2015        PMID: 25964308      PMCID: PMC4527037          DOI: 10.2215/CJN.12181214

Source DB:  PubMed          Journal:  Clin J Am Soc Nephrol        ISSN: 1555-9041            Impact factor:   8.237


  43 in total

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4.  Iron chelation with deferasirox in adult and pediatric patients with thalassemia major: efficacy and safety during 5 years' follow-up.

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6.  Equations to estimate creatinine excretion rate: the CKD epidemiology collaboration.

Authors:  Joachim H Ix; Christina L Wassel; Lesley A Stevens; Gerald J Beck; Marc Froissart; Gerjan Navis; Roger Rodby; Vicente E Torres; Yaping Lucy Zhang; Tom Greene; Andrew S Levey
Journal:  Clin J Am Soc Nephrol       Date:  2010-10-21       Impact factor: 8.237

Review 7.  Renal complications in transfusion-dependent beta thalassaemia.

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8.  Renal dysfunction in patients with thalassaemia.

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9.  The use of plasma creatinine concentration for estimating glomerular filtration rate in infants, children, and adolescents.

Authors:  G J Schwartz; L P Brion; A Spitzer
Journal:  Pediatr Clin North Am       Date:  1987-06       Impact factor: 3.278

10.  A new equation to estimate glomerular filtration rate.

Authors:  Andrew S Levey; Lesley A Stevens; Christopher H Schmid; Yaping Lucy Zhang; Alejandro F Castro; Harold I Feldman; John W Kusek; Paul Eggers; Frederick Van Lente; Tom Greene; Josef Coresh
Journal:  Ann Intern Med       Date:  2009-05-05       Impact factor: 25.391

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1.  Renal Hemosiderosis among Iranian Transfusion Dependent β-Thalassemia Major Patients.

Authors:  Mozhgan Hashemieh; Mitra Radfar; Azita Azarkeivan; Seyed Mohammad Taghi Hosseini Tabatabaei; Sedigheh Nikbakht; Mehdi Yaseri; Kourosh Sheibani
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