Congenital hyponychia of the hands with lymphangiectases: a new entity?

We present a case of 58-year-old woman with congenital hyponychia of the ten fingers and oedema of the fingertips as the only cutaneous alterations. There was no associated systemic condition or additional ectodermal abnormality. The biopsy showed lymphangiectases mainly confined to the papillary dermis but also in the reticular dermis. We propose the designation "congenital hyponychia of the hands with lymphangiectases" for this apparently not previously described condition.