Literature DB >> 25949451

Doxycycline for haematopoietic stem cell transplantation-related thrombotic microangiopathy.

Hassane Izzedine1, Alain Baumelou1, Chems Gharbi1, Edward Bourry1, Jean Paul Vernant2.   

Abstract

Entities:  

Year:  2010        PMID: 25949451      PMCID: PMC4421533          DOI: 10.1093/ndtplus/sfq072

Source DB:  PubMed          Journal:  NDT Plus        ISSN: 1753-0784


× No keyword cloud information.
Transplantation-associated thrombotic microangiopathy (TA-TMA) is a devastating consequence of allogeneic haematopoietic stem cell transplantation (HSCT) with a mortality rate of 60–90%. None of the interventions used, as used up till now in idiopathic thrombotic thrombocytopaenic purpura (TTP) (fresh frozen plasma transfusion, plasma exchange and steroids), were effective to treat TA-TMA [1,2]. We report a dramatic improvement of TA-TMA in two HSCT patients [conditioning, cyclophosphamide, total body irradiation, graft-versus-host disease (GVHD) prophylaxis] using doxycycline. A 36-year-old woman with Hodgkin's lymphoma received an allogeneic HSCT in December 2002. Twelve months later, she developed a biopsy-proven TMA (proteinuria, 3 g/day, microscopic haematuria, oliguric acute renal failure with creatinine level at 680 µmol/L; haemoglobin Hb, 6.3 g/dL; schistocytes; platelet count, 35 × 109/L; LDH, 1754 IU/L). The serum complement proteins were at normal levels, no mutations of the membrane cofactor protein were found and a plasma ADAMTS13 activity was found at 40%. Steroids, plasma exchange, fresh frozen plasma transfusion, vincristine and haemodialysis were tried with a partial response (haemoglobin, 7.3 g/dL, platelet 70 000/mm3 both after treatment). Doxycycline 200 mg daily was added for a suspected gastrointestinal Bartonella infection. Within two months, haemoglobin and platelet count rose without transfusion to 10.8 g/dL and 234 000/mm3, respectively. Despite improvement of haematological parameters, the patient remained dialysis-dependent. The second patient had a similar haematologic disease and course under doxycycline prescribed for a bartholinitis. Five patients with TTP and Bartonella-like erythrocyte inclusions, successfully treated with doxycycline, experienced recurrence of their TTP following cessation of treatment [3]. TA-TMA has a multi-factorial aetiology of endothelial damage. Doxycycline targeting the adherens junction on endothelial cells prevents vascular hyperpermeability [4]. Doxycycline as a potential treatment of TA-TMA warrants further studies. Conflict of interest statement. None declared.
  4 in total

1.  Bartonella-like erythrocyte inclusions in thrombotic thrombocytopenic purpura.

Authors:  S R Tarantolo; J D Landmark; P C Iwen; A Kessinger; W C Chan; S H Hinrichs
Journal:  Lancet       Date:  1997-11-29       Impact factor: 79.321

2.  Doxycycline induces membrane expression of VE-cadherin on endothelial cells and prevents vascular hyperpermeability.

Authors:  Ofer Fainaru; Irit Adini; Ofra Benny; Lauren Bazinet; Elke Pravda; Robert D'Amato; Judah Folkman
Journal:  FASEB J       Date:  2008-07-07       Impact factor: 5.191

Review 3.  Thrombotic microangiopathy in haematopoietic stem cell transplantation: diagnosis and treatment.

Authors:  Cecilia M Choi; Alvin H Schmaier; Michael R Snell; Hillard M Lazarus
Journal:  Drugs       Date:  2009       Impact factor: 9.546

Review 4.  Interventions for haemolytic uraemic syndrome and thrombotic thrombocytopenic purpura.

Authors:  Mini Michael; Elizabeth J Elliott; Greta F Ridley; Elisabeth M Hodson; Jonathan C Craig
Journal:  Cochrane Database Syst Rev       Date:  2009-01-21
  4 in total

北京卡尤迪生物科技股份有限公司 © 2022-2023.