| Literature DB >> 25930183 |
Maike Rohr1,2, Thomas Kohnen1, Burkhard von Jagow3,4.
Abstract
BACKGROUND: The IgG4-related disease describes a new multisystem disorder, which can also be manifested in the orbit. This syndrome is characterized by a multifocal chronic fibroinflammation with high levels of plasma cells expressing IgG4. CASE REPORT: This article reports the case of a patient with advanced bilateral tumors of the upper eyelid and orbit. The diagnosis of IgG4-related disease was only revealed after many years and after many biopsies of the tumors had been carried out. The initiation of a systemic steroid therapy led to a rapid reduction of the tumors and an improvement in the general condition of the patient.Entities:
Keywords: Fibroinflammatory disease; Lacrimal glands; Multisystem disease; Plasma cells; Systemic steroids
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Year: 2015 PMID： 25930183 DOI： 10.1007/s00347-015-0008-8
Source DB: PubMed Journal: Ophthalmologe ISSN： 0941-293X Impact factor: 1.059