Literature DB >> 25804045

[Nephrotic syndrome in a female patient with Rapunzel syndrome].

N S Umbetalina, E M Turgunov, L G Turgunova, T A Baesheva, I V Bacheva.   

Abstract

The Rapunzel syndrome is a rare complication of gastric trichobezoar, which may be long insidious. Systemic hair eating gradually leads to bezoar growth, gastritis, gastric mucosal ulcerations, and evacuatory disorders. The Rapunzel syndrome may cause acute and chronic bowel obstruction, peritonitis, pancreatitis, appendicitis, anemia, hypoalbuminemia, and allergic manifestations. Neither proteinuria nor nephrotic syndrome is depicted in any of the 38 Rapunzel syndrome cases described in the literature. The authors present the first case of gastric trichobezoar extending to the small bowel (its total length was 118 cm), which gave rise to chronic recurrent partial bowel obstruction, causing intoxication nephrotic syndrome in a 20-year-old women with trichotillomania. The nephrotic syndrome became a reason for her admission to a nephrology department and had specific features: it was unaccompanied by hypercholesterolemia, it rapidly regressed and completely disappeared after surgical removal of the trichobezoar weighing 1980 g.

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Year:  2014        PMID: 25804045     DOI: 10.17116/terarkh2014861278-80

Source DB:  PubMed          Journal:  Ter Arkh        ISSN: 0040-3660            Impact factor:   0.467


  3 in total

1.  Formation of a temporary gastrostomy to aid delivery of gastric trichobezoar and decrease incidence of wound infection.

Authors:  Ahmed AbdElhamid Darwish; Abdelghany Em Abdelgawad; Esther Platt; Robin Garrett-Cox
Journal:  BMJ Case Rep       Date:  2019-06-21

2.  Rapunzel syndrome: a rare cause of hypoproteinaemia and review of literature.

Authors:  Waqas Ullah; Kaiser Saleem; Ejaz Ahmad; Faiz Anwer
Journal:  BMJ Case Rep       Date:  2016-09-26

3.  Trichobezoar presenting as a gastric outlet obstruction: A case report.

Authors:  Eugene Nwankwo; Edward Daniele; Erin Woller; John Fitzwater; Thomas McGill; Steven E Brooks
Journal:  Int J Surg Case Rep       Date:  2017-03-16
  3 in total

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