Literature DB >> 25755194

Infant pulmonary function testing in chronic pneumonitis of infancy due to surfactant protein C mutation.

Avigdor Hevroni1, Aliza Goldman1, Chaim Springer1.   

Abstract

Pulmonary function testing is a vital tool in evaluation and management of adult ILD patients and is rarely overlooked during workup. However, there is paucity of data regarding its usefulness in management of infants with suspected interstitial lung disease. In this paper, we present the contribution of infant pulmonary function testing (iPFT) to the management of two infants with biopsy confirmed chronic pneumonitis of infancy due to surfactant protein C mutation. We have productively and safely used serial iPFT for decision making both during diagnosis and follow-up of these infants. This article is protected by copyright. All rights reserved.

Entities:  

Keywords:  child interstitial lung disease (chILD); chronic pneumonitis of infancy (CPI); diffuse lung disease (DLD); infant pulmonary function testing (iPFT); surfactant protein C deficiency (SFTPC)

Mesh:

Substances:

Year:  2015        PMID: 25755194     DOI: 10.1002/ppul.23166

Source DB:  PubMed          Journal:  Pediatr Pulmonol        ISSN: 1099-0496


  2 in total

1.  Mediastinal lymphadenopathy reflecting disease activity in an infant with chronic pneumonitis of infancy associated with surfactant protein C mutation: a case report and literature review.

Authors:  Sang Hoon Lee; Young Ok Kim; Eun Lee; In Seok Jeong; Yoo-Duk Choi; Hwa Jin Cho
Journal:  J Thorac Dis       Date:  2018-10       Impact factor: 2.895

Review 2.  Alveolar Dynamics and Beyond - The Importance of Surfactant Protein C and Cholesterol in Lung Homeostasis and Fibrosis.

Authors:  Kirsten Sehlmeyer; Jannik Ruwisch; Nuria Roldan; Elena Lopez-Rodriguez
Journal:  Front Physiol       Date:  2020-05-05       Impact factor: 4.566

  2 in total

北京卡尤迪生物科技股份有限公司 © 2022-2023.