Literature DB >> 25743388

Multimodal treatment of abdominal and pelvic desmoplastic small round cell tumor with relative good prognosis.

Yuhong Tang1, Hualin Song2, Yali Bao3, Yang Zhi4.   

Abstract

OBJECTIVE: To investigate the clinicopathologic features and survival outcomes of desmoplastic small round cell tumor (DSCRT).
METHODS: The retrospective cohort study was performed on clinical and pathological data of 18 DSCRT patients. Among them, two subgroups were classified according to treatment modalities. 10 cases underwent operation and adjuvant chemotherapy (group 1, 10/18, 55.6%) and 8 cases were diagnosed by fine needle aspiration biopsy without surgical intervention (group 2, 8/18, 44.4%). All cases received six courses of multiple agents chemotherapy.
RESULTS: All cases were histologically confirmed as DSRCT and Cox regression revealed that sex, tumor localization and treatment modality affected patient outcomes. Kaplan-Meier analysis revealed that the median survival time was 22.0 ± 4.0 mo in group 1 versus 9.0 ± 0.7 mo in group 2.
CONCLUSION: DSRCT is highly aggressive malignance with poor prognosis, surgical excision with combination of chemotherapy can significantly improve the survival outcomes.
Copyright © 2015 Surgical Associates Ltd. Published by Elsevier Ltd. All rights reserved.

Entities:  

Keywords:  Chemotherapy; Desmoplastic small round cell tumor; Diagnosis; Prognosis; Surgery

Mesh:

Year:  2015        PMID: 25743388     DOI: 10.1016/j.ijsu.2015.02.015

Source DB:  PubMed          Journal:  Int J Surg        ISSN: 1743-9159            Impact factor:   6.071


  3 in total

Review 1.  Desmoplastic small round-cell tumour of the peritoneal cavity: case report and literature review.

Authors:  N Tsoukalas; M Kiakou; G Nakos; M Tolia; M Galanopoulos; K Tsapakidis; K Kamposioras; C Christofyllakis; G Dimitrakopoulos; D Sambaziotis
Journal:  Ann R Coll Surg Engl       Date:  2020-01-24       Impact factor: 1.891

Review 2.  High-Dose Chemotherapy with Stem Cell Rescue in Desmoplastic Small Round Cell Tumor: A Single-Institution Experience and Review of the Literature.

Authors:  Kayleen Bailey; Michael Roth; Daniel Weiser; Jonathan Gill
Journal:  Sarcoma       Date:  2018-05-06

3.  Clinical Characteristics, Management, and Outcomes of 19 Nonpediatric Patients with Desmoplastic Small Round Cell Tumor: A Cohort of Brazilian Patients.

Authors:  Fernando Campos; Daniel L Coutinho; Maria Letícia G Silva; Ademar Lopes; Antônio Nascimento; Samuel Aguiar Júnior; Ulisses R Nicolau; Maria Nirvana Formiga; Felipe D'Almeida Costa; Celso Mello
Journal:  Sarcoma       Date:  2020-10-28
  3 in total

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