Literature DB >> 25664015

Left ventricular noncompaction cardiomyopathy: a case report and literature review.

Ying-Nan Lin1, Yu-Qiang Wang1, Yi Yu2, Qing Cao1, Fei Wang1, Shu-Yan Chen1.   

Abstract

Left ventricular noncompaction cardiomyopathy (LVNC) is a relatively rare congenital disorder prominently characterized by prominent trabeculations and intertrabecular recesses that communicate with the ventricular cavity rather than the coronary circulation. LVNC can occur in isolation or coexist with other cardiac and/or systemic anomalies, in especial neuromuscular disorders. The clinical presentation varies ranging from asymptomatic patients to patients who develop ventricular arrhythmias, thromboembolism, heart failure and sudden cardiac death. Although LVNC is commonly diagnosed by echocardiography, there are also other useful diagnostic techniques, including contrast ventriculography, CT and MRI. Now, it is being diagnosed more frequently in patients of all ages because of increased awareness and improvements in imaging methods. We described the case of a woman who presented with heart failure for the first time at 62 years of age. The diagnosis was LVNC. Transthoracic echocardiography showed a trabeculated, sponge-like appearance of the ventricular apical and inferolateral segments. After medical management, the patient was asymptomatic at the 1-month follow-up examination. Now we discussed the diagnosis of this case and reviewed the medical literature that pertained to LVNC.

Entities:  

Keywords:  Trabeculations; congestive heart failure; left ventricular noncompaction cardiomyopathy

Year:  2014        PMID: 25664015      PMCID: PMC4307462     

Source DB:  PubMed          Journal:  Int J Clin Exp Med        ISSN: 1940-5901


  15 in total

1.  [III Brazilian Guidelines on Chronic Heart Failure].

Authors:  Edimar Alcides Bocchi; Fabiana Goulart Marcondes Braga; Silvia Moreira Ayub Ferreira; Luis Eduardo Paim Rohde; Wilson Alves de Oliveira; Dirceu Rodrigues de Almeida; Maria da Consolação Vieira Moreira; Reinaldo Bulgarelli Bestetti; Solange Bordignon; Clério Azevedo; Evandro Mesquita Tinoco; Ricardo Mourilhe Rocha; Victor Sarli Issa; Almir Ferraz; Fátima das Dores Cruz; Guilherme Veiga Guimarães; Vanessa Dos Santos Pereira Montera; Denilson Campos Albuquerque; Fernando Bacal; Germano Emilio Conceição Souza; João Manoel Rossi Neto; Nadine Oliveira Clausell; Silvia Marinho Martins; Alexandre Siciliano; João David de Souza Neto; Luis Felipe Moreira; Ricardo Alkmim Teixeira; Lídia Zytynski Moura; Luís Beck-da-Silva; Salvador Rassi; Estela Azeka; Estela Horowitz; Felix Ramires; Marcus Vinicius Simões; Renato Barroso Pereira de Castro; Vera Maria Cury Salemi; Humberto Villacorta Junior; José Henrique Vila; Ricardo Simões; Francisco Albanesi; Marcelo Westerlund Montera
Journal:  Arq Bras Cardiol       Date:  2009       Impact factor: 2.000

2.  Natural history and familial characteristics of isolated left ventricular non-compaction.

Authors:  Ross T Murphy; Rajesh Thaman; Juan Gimeno Blanes; Deirdre Ward; Elias Sevdalis; Efi Papra; Anatoli Kiotsekoglou; Anatoli Kiotsekolglou; Maria T Tome; Denis Pellerin; William J McKenna; Perry M Elliott
Journal:  Eur Heart J       Date:  2004-11-30       Impact factor: 29.983

Review 3.  The morphological spectrum of ventricular noncompaction.

Authors:  Robert M Freedom; Shi-Joon Yoo; Don Perrin; Glenn Taylor; Steffen Petersen; Robert H Anderson
Journal:  Cardiol Young       Date:  2005-08       Impact factor: 1.093

Review 4.  Left ventricular non-compaction revisited: a distinct phenotype with genetic heterogeneity?

Authors:  Erwin Oechslin; Rolf Jenni
Journal:  Eur Heart J       Date:  2011-01-31       Impact factor: 29.983

5.  Validation of noncompaction criteria in dilated cardiomyopathy, and valvular and hypertensive heart disease.

Authors:  Barbara S Frischknecht; Christine H Attenhofer Jost; Erwin N Oechslin; Burkhardt Seifert; Philipp Hoigné; Malgorzata Roos; Rolf Jenni
Journal:  J Am Soc Echocardiogr       Date:  2005-08       Impact factor: 5.251

6.  Predictors of adverse outcome in adolescents and adults with isolated left ventricular noncompaction.

Authors:  Matthias Greutmann; May Ling Mah; Candice K Silversides; Sabine Klaassen; Christine H Attenhofer Jost; Rolf Jenni; Erwin N Oechslin
Journal:  Am J Cardiol       Date:  2011-10-28       Impact factor: 2.778

Review 7.  Isolated noncompaction of the left ventricular myocardium in adults: a systematic overview.

Authors:  Nisha L Bhatia; A Jamil Tajik; Susan Wilansky; D Eric Steidley; Farouk Mookadam
Journal:  J Card Fail       Date:  2011-09       Impact factor: 5.712

Review 8.  Isolated left ventricular noncompaction in a 90-year-old man.

Authors:  Cihan Cevik; Raymond F Stainback
Journal:  Tex Heart Inst J       Date:  2012

9.  Isolated noncompaction of left ventricular myocardium. A study of eight cases.

Authors:  T K Chin; J K Perloff; R G Williams; K Jue; R Mohrmann
Journal:  Circulation       Date:  1990-08       Impact factor: 29.690

Review 10.  Left ventricular noncompaction cardiomyopathy: updated review.

Authors:  Dioma U Udeoji; Kiran J Philip; Ryan P Morrissey; Anita Phan; Ernst R Schwarz
Journal:  Ther Adv Cardiovasc Dis       Date:  2013-10
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  2 in total

1.  Coexistence of hypertrophic cardiomyopathy and left ventricular non-compaction cardiomyopathy-a description of two cases.

Authors:  Sara Kochańska; Michał Spałek; Grzegorz Wróbel; Wioletta Korzeluch; Ilona Michałowska; Tadeusz Kuder; Beata Wożakowska-Kapłon
Journal:  Quant Imaging Med Surg       Date:  2022-07

Review 2.  Concise Review: Precision Matchmaking: Induced Pluripotent Stem Cells Meet Cardio-Oncology.

Authors:  Pooja Nair; Maricela Prado; Isaac Perea-Gil; Ioannis Karakikes
Journal:  Stem Cells Transl Med       Date:  2019-04-24       Impact factor: 6.940

  2 in total

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