Literature DB >> 25653933

Occipital meningoencephalocele with Cleft Lip, Cleft Palate and Limb Abnormalities- A Case Report.

Arthi Ganapathy1, Sadeesh T1, Mary Hydrina Swer1, Sudha Rao2.   

Abstract

A 21-week-old still born female fetus with occipital encepholocele, cleft lip and cleft palate was received from the Department of Obstetrics and Gynecology, Mahatma Gandhi Medical College and Research Institute, Pondicherry and was studied in detail. It was born to Primigravida, of a second degree consanguineous marriage, with unremarkable family history. The biometric measurements were noted which corresponded to the age of the fetus. Further the fetus was embalmed and dissected. On examination an encephalocele of 2.7×1.5 cm was seen in the occipital region with a midline defect in the occipital bone and herniated brain tissue. Other anomalies observed were right unilateral cleft lip, right cleft palate, and bilateral syndactyly of the lower limbs and associated Congenital Talipus Equino Varus of the right foot. Other internal organs were developed appropriate for the age of the fetus.

Entities:  

Keywords:  Cleft lip; Cleft palate; Congenital talipes equino varus; Occipital meningoencephalocele; Syndactyly; Ultrasonogram

Year:  2014        PMID: 25653933      PMCID: PMC4316239          DOI: 10.7860/JCDR/2014/10842.5326

Source DB:  PubMed          Journal:  J Clin Diagn Res        ISSN: 0973-709X


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