Literature DB >> 25584260

Mesenteric fibromatosis (desmoid tumour) - a rare case report.

Mukut D1, Hemanth Sureshwara Ghalige2, Santhosh R3, M Birkumar Sharma4, Th Sudhir Chandra Singh4.   

Abstract

Mesenteric Fibromatosis (MF) is a proliferative fibroblastic lesion of small intestinal mesentery. It constitutes 8% of all desmoid tumours, which represent 0.03% of all neoplasm. It is histologically benign but may invade locally and recur after excision. It occurs sporadically or in association with Familial adenomatous polyposis (FAP) mutation as a component of Gardner's syndrome. The presenting features of MF are asymptomatic abdominal mass, abdominal discomfort or pain, bowel or ureteral obstruction, intestinal perforation, fistula, functional impairment of ileoanal anastomosis following colectomy in FAP cases. A 29-year-old male presented with a swelling on the right side of the umbilicus for six months and dull aching pain for two months. Fine needle aspiration cytology, ultrasonography, contrast enhanced computerized tomography findings were inconclusive. After Exploratory laparotomy, a mass approx 6x5x4 cm in ileal mesentery was identified and excised along with 20cm of ileum. End to end anastomosis was done and specimen was sent for histopathology which confirmed the diagnosis of MF. Considering the rarity of this tumour and difficulties in diagnostic and therapeutic ambit, we believe it is justified to describe this case which came to our observation.

Entities:  

Keywords:  Desmoid tumour; Gardner’s syndrome; Mesenteric fibromatosis

Year:  2014        PMID: 25584260      PMCID: PMC4290279          DOI: 10.7860/JCDR/2014/8520.5098

Source DB:  PubMed          Journal:  J Clin Diagn Res        ISSN: 0973-709X


  5 in total

Review 1.  Gardner's syndrome: a case report and review of the literature.

Authors:  C Fotiadis; D-K Tsekouras; P Antonakis; J Sfiniadakis; M Genetzakis; G-C Zografos
Journal:  World J Gastroenterol       Date:  2005-09-14       Impact factor: 5.742

Review 2.  Radiotherapy is effective for desmoid tumors (aggressive fibromatosis) - long-term results of a German multicenter study.

Authors:  Jan Kriz; Hans Theodor Eich; Uwe Haverkamp; M Heinrich Seegenschmiedt; Jürgen Heide; Frank Bruns; Oliver Micke
Journal:  Oncol Res Treat       Date:  2014-04-14       Impact factor: 2.825

3.  Mesenteric fibromatosis. Case report.

Authors:  A Giuliani; M Demoro; A Ciardi; M Scimó; F Galati; M T Lonardo; G Galati
Journal:  J Exp Clin Cancer Res       Date:  2007-09

4.  A giant mesenteric fibromatosis case presenting with mechanical intestinal obstruction and successfully resected with partial duodeno-jejunectomy and right hemicolectomy.

Authors:  Coskun Polat; Fatma Aktepe; Serkan Turel; Burc Yazicioglu; Taner Ozkececi; Yuksel Arikan
Journal:  Clinics (Sao Paulo)       Date:  2010       Impact factor: 2.365

5.  Multiple desmoid tumors in a patient with Gardner's syndrome - Report of a case.

Authors:  Lílian Vital Pinheiro; João José Fagundes; Cláudio Saddy Rodrigues Coy; Cesar Cabello; Ivan Toro; Marcelo Michellino; Paulo Henrique Fachina; Marc Ward; Raquel Franco Leal; Maria de Lourdes Setsuko Ayrizono
Journal:  Int J Surg Case Rep       Date:  2014-04-18
  5 in total
  3 in total

1.  Primary Desmoid-Type Fibromatosis of the Mesentery: Report of an Unusual Tumor Localization.

Authors:  Mohamed Allaoui; Mohamed Tarchouli; Adil Boudhas; Reda El Ochi; Ahmed Bounaim; Abderrahmane Al Bouzidi; Mohamed Oukabli
Journal:  J Gastrointest Cancer       Date:  2018-03

2.  Ball in the Wall: Mesenteric Fibromatosis-a Rare Case Report.

Authors:  Abhinav Deshpande; Ankita Tamhane; Y S Deshpande; Radhika Pagey; Meena Pangarkar
Journal:  Indian J Surg Oncol       Date:  2020-04-25

Review 3.  Desmoid Tumor as an Initial Presentation of Familial Adenomatous Polyposis: A Review of the Literature.

Authors:  Fady G Haddad; Sandy El Bitar; Iskandar Barakat; Liliane Deeb
Journal:  Cureus       Date:  2018-03-09
  3 in total

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