Literature DB >> 25575846

A case of variably protease-sensitive prionopathy treated with doxycyclin.

Hamid Assar1, Raffi Topakian2, Serge Weis3, Jasmin Rahimi4, Johannes Trenkler5, Romana Höftberger4, Fahmy Aboulenein-Djamshidian6, Thomas Ströbel4, Herbert Budka7, Helen Yull8, Mark W Head8, James W Ironside8, Gabor G Kovacs4.   

Abstract

Entities:  

Keywords:  CREUTZFELDT-JAKOB DISEASE; HISTOPATHOLOGY; NEUROPATHOLOGY; POST MORTEM; PRION

Mesh:

Substances:

Year:  2015        PMID: 25575846     DOI: 10.1136/jnnp-2014-309871

Source DB:  PubMed          Journal:  J Neurol Neurosurg Psychiatry        ISSN: 0022-3050            Impact factor:   10.154


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  10 in total

Review 1.  Prion protein scrapie and the normal cellular prion protein.

Authors:  Caroline J Atkinson; Kai Zhang; Alan L Munn; Adrian Wiegmans; Ming Q Wei
Journal:  Prion       Date:  2016       Impact factor: 3.931

Review 2.  Variably protease-sensitive prionopathy: A differential diagnostic consideration for dementia.

Authors:  Stella H Kim; Melissa M Yu; Adriana M Strutt
Journal:  Neurol Clin Pract       Date:  2019-04

3.  Preventive study in subjects at risk of fatal familial insomnia: Innovative approach to rare diseases.

Authors:  Gianluigi Forloni; Mauro Tettamanti; Ugo Lucca; Yasmin Albanese; Elena Quaglio; Roberto Chiesa; Alessandra Erbetta; Flavio Villani; Veronica Redaelli; Fabrizio Tagliavini; Vladimiro Artuso; Ignazio Roiter
Journal:  Prion       Date:  2015       Impact factor: 3.931

4.  Variably Protease-sensitive Prionopathy in a Middle-aged Man With Rapidly Progressive Dementia.

Authors:  Juebin Huang; Mark Cohen; Jiri Safar; Alexander P Auchus
Journal:  Cogn Behav Neurol       Date:  2021-09-02       Impact factor: 1.590

5.  Prion-specific and surrogate CSF biomarkers in Creutzfeldt-Jakob disease: diagnostic accuracy in relation to molecular subtypes and analysis of neuropathological correlates of p-tau and Aβ42 levels.

Authors:  Francesca Lattanzio; Samir Abu-Rumeileh; Alessia Franceschini; Hideaki Kai; Giulia Amore; Ilaria Poggiolini; Marcello Rossi; Simone Baiardi; Lynne McGuire; Anna Ladogana; Maurizio Pocchiari; Alison Green; Sabina Capellari; Piero Parchi
Journal:  Acta Neuropathol       Date:  2017-02-15       Impact factor: 17.088

6.  Doxycycline in early CJD: a double-blinded randomised phase II and observational study.

Authors:  Daniela Varges; Henrike Manthey; Uta Heinemann; Claudia Ponto; Matthias Schmitz; Walter J Schulz-Schaeffer; Anna Krasnianski; Maren Breithaupt; Fabian Fincke; Katharina Kramer; Tim Friede; Inga Zerr
Journal:  J Neurol Neurosurg Psychiatry       Date:  2016-11-02       Impact factor: 10.154

7.  Neuroprotective Effects of Doxycycline in the R6/2 Mouse Model of Huntington's Disease.

Authors:  Emanuela Paldino; Claudia Balducci; Pietro La Vitola; Luisa Artioli; Vincenza D'Angelo; Carmela Giampà; Vladimiro Artuso; Gianluigi Forloni; Francesca R Fusco
Journal:  Mol Neurobiol       Date:  2019-12-26       Impact factor: 5.590

8.  Variably protease-sensitive prionopathy mimicking frontotemporal dementia.

Authors:  Miren Aizpurua; Sashika Selvackadunco; Helen Yull; Christopher M Kipps; James W Ironside; Istvan Bodi
Journal:  Neuropathology       Date:  2019-03-07       Impact factor: 1.906

Review 9.  The Use of Real-Time Quaking-Induced Conversion for the Diagnosis of Human Prion Diseases.

Authors:  Anna Poleggi; Simone Baiardi; Anna Ladogana; Piero Parchi
Journal:  Front Aging Neurosci       Date:  2022-04-25       Impact factor: 5.750

10.  Small heterodimer partner (SHP) aggravates ER stress in Parkinson's disease-linked LRRK2 mutant astrocyte by regulating XBP1 SUMOylation.

Authors:  Jee Hoon Lee; Ji-Hye Han; Eun-Hye Joe; Ilo Jou
Journal:  J Biomed Sci       Date:  2021-07-07       Impact factor: 8.410

  10 in total

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