Literature DB >> 25478934

Metabolic and adipose tissue signatures in adults with Prader-Willi syndrome: a model of extreme adiposity.

Delphine Lacroix1, Sandrine Moutel, Muriel Coupaye, Hélène Huvenne, Pauline Faucher, Véronique Pelloux, Christine Rouault, Jean-Philippe Bastard, Nicolas Cagnard, Béatrice Dubern, Karine Clément, Christine Poitou.   

Abstract

CONTEXT: Prader-Willi syndrome (PWS), the most frequent syndrome of obesity, is a model of early fat mass (FM) development, but scarce data exist on adipose tissue characteristics.
OBJECTIVE: The objective of the study was to compare metabolic, fat distribution, and transcriptomic signatures of sc adipose tissue (scAT) in PWS adults, with matched obese adults with primary obesities. MAIN OUTCOMES AND MEASURES: Hormonal and metabolic assessments, systemic inflammation, and gene expression in scAT were compared between PWS patients and obese controls (OCs). Each 42nd PWS patient was matched with one randomly paired control with primary obesity. Matching factors were age, gender, fat mass (percentage), and diabetic status.
RESULTS: Compared with OCs, the PWS group had a decreased percentage of trunk FM and a better metabolic profile with decreased insulin and homeostasis model assessment, an index of insulin-resistance, and increased concentrations of serum adiponectin and ghrelin. Adipocyte size relative to body fat was significantly higher in PWS vs OCs. scAT in PWS patients was characterized by a transcriptomic functional signature with enrichment of themes related to immunoinflammation, the extracellular matrix, and angiogenesis. A RT-PCR targeted study revealed that candidate genes encoding proinflammatory markers and remodeling molecules, CD68, CD3e, IL-1β, chemokine (C-C motif) ligand 5, collagen type 4-α, and lysyl oxidase, were down-regulated.
CONCLUSION: Matched for FM, PWS subjects have a better metabolic profile, a phenotype that could be linked to changes in scAT remodeling and promotion of adipocyte growth.

Entities:  

Mesh:

Year:  2014        PMID: 25478934     DOI: 10.1210/jc.2014-3127

Source DB:  PubMed          Journal:  J Clin Endocrinol Metab        ISSN: 0021-972X            Impact factor:   5.958


  13 in total

Review 1.  Update on Diabetes Mellitus and Glucose Metabolism Alterations in Prader-Willi Syndrome.

Authors:  Antonino Crinò; Graziano Grugni
Journal:  Curr Diab Rep       Date:  2020-02-06       Impact factor: 4.810

Review 2.  Prader-Willi Syndrome in Adults: An Update On Nutritional Treatment and Pharmacological Approach.

Authors:  Silvia Savastano; Giovanna Muscogiuri; Luigi Barrea; Claudia Vetrani; Danilo Fintini; Giulia de Alteriis; Filippo Maria Panfili; Sarah Bocchini; Ludovica Verde; Annamaria Colao
Journal:  Curr Obes Rep       Date:  2022-09-05

3.  Circulating Irisin in Children and Adolescents With Prader-Willi Syndrome: Relation With Glucose Metabolism.

Authors:  Stefania Mai; Danilo Fintini; Chiara Mele; Alessio Convertino; Sarah Bocchini; Graziano Grugni; Gianluca Aimaretti; Roberta Vietti; Massimo Scacchi; Antonino Crinò; Paolo Marzullo
Journal:  Front Endocrinol (Lausanne)       Date:  2022-06-14       Impact factor: 6.055

Review 4.  Prader Willi Syndrome: Genetics, Metabolomics, Hormonal Function, and New Approaches to Therapy.

Authors:  Krystal A Irizarry; Mark Miller; Michael Freemark; Andrea M Haqq
Journal:  Adv Pediatr       Date:  2016-08

5.  Angiopoietin-like 8 (ANGPTL8) as a potential predictor of NAFLD in paediatric patients with Prader-Willi Syndrome.

Authors:  C Mele; A Crinò; D Fintini; S Mai; A Convertino; S Bocchini; P Di Paolo; G Grugni; G Aimaretti; M Scacchi; P Marzullo
Journal:  J Endocrinol Invest       Date:  2020-10-16       Impact factor: 4.256

6.  Dietary Modulation of Gut Microbiota Contributes to Alleviation of Both Genetic and Simple Obesity in Children.

Authors:  Chenhong Zhang; Aihua Yin; Hongde Li; Ruirui Wang; Guojun Wu; Jian Shen; Menghui Zhang; Linghua Wang; Yaping Hou; Haimei Ouyang; Yan Zhang; Yinan Zheng; Jicheng Wang; Xiaofei Lv; Yulan Wang; Feng Zhang; Benhua Zeng; Wenxia Li; Feiyan Yan; Yufeng Zhao; Xiaoyan Pang; Xiaojun Zhang; Huaqing Fu; Feng Chen; Naisi Zhao; Bruce R Hamaker; Laura C Bridgewater; David Weinkove; Karine Clement; Joel Dore; Elaine Holmes; Huasheng Xiao; Guoping Zhao; Shengli Yang; Peer Bork; Jeremy K Nicholson; Hong Wei; Huiru Tang; Xiaozhuang Zhang; Liping Zhao
Journal:  EBioMedicine       Date:  2015-07-10       Impact factor: 8.143

7.  Circulating angiopoietin-like 8 (ANGPTL8) is a marker of liver steatosis and is negatively regulated by Prader-Willi Syndrome.

Authors:  Chiara Mele; Graziano Grugni; Stefania Mai; Roberta Vietti; Gianluca Aimaretti; Massimo Scacchi; Paolo Marzullo
Journal:  Sci Rep       Date:  2017-06-09       Impact factor: 4.379

8.  Gut microbiota of obese subjects with Prader-Willi syndrome is linked to metabolic health.

Authors:  Lisa M Olsson; Christine Poitou; Valentina Tremaroli; Muriel Coupaye; Judith Aron-Wisnewsky; Fredrik Bäckhed; Karine Clément; Robert Caesar
Journal:  Gut       Date:  2019-10-14       Impact factor: 23.059

9.  Differences in circulating microRNA signature in Prader-Willi syndrome and non-syndromic obesity.

Authors:  Devis Pascut; Sofia Tamini; Silvia Bresolin; Pablo Giraudi; Giuseppe Basso; Alessandro Minocci; Claudio Tiribelli; Graziano Grugni; Alessandro Sartorio
Journal:  Endocr Connect       Date:  2018-12-01       Impact factor: 3.335

10.  Fat-Free Mass Is Better Related to Serum Uric Acid Than Metabolic Homeostasis in Prader-Willi Syndrome.

Authors:  Paolo Marzullo; Chiara Mele; Alessandro Minocci; Stefania Mai; Massimo Scacchi; Alessandro Sartorio; Gianluca Aimaretti; Graziano Grugni
Journal:  Nutrients       Date:  2020-08-25       Impact factor: 5.717

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