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Literature DB >> 2546356

Polyglucosan bodies in intramuscular motor nerves.

R A Bernsen¹, H L Busard, H J Ter Laak, F J Gabreëls, W O Renier, E M Joosten, A G Theeuwes.

Abstract

The presence of polyglucosan bodies was studied in intramuscular motor nerves of 292 muscle biopsies. These biopsies were classified into five diagnostic categories and investigated for the presence of polyglucosan bodies in relation to age and sex. Their presence was nonspecific in patients over 20 years, the only correlation being with ageing. Under 20 years, their presence pointed to the diagnosis of Lafora's disease. In cases in which both a muscle biopsy and a sural nerve biopsy were performed, the former appeared to contain these polyglucosans more frequently.

Entities: Chemical Disease Species

Mesh：

Substances：
Polysaccharides
Glucose

Year: 1989 PMID： 2546356 DOI： 10.1007/BF00687891

Source DB: PubMed Journal: Acta Neuropathol ISSN： 0001-6322 Impact factor: 17.088

40 in total

1. Progressive familial myoclonic epilepsy in three families: its clinical features and pathological basis.

Authors: D G HARRIMAN; J H MILLAR; A C STEVENSON
Journal: Brain Date: 1955-09 Impact factor: 13.501

2. Corpora amylacea of the lumbar spinal cord and peripheral nervous system.

Authors: P Averback; H Langevin
Journal: Arch Neurol Date: 1978-02

3. Lafora's disease. Comparison of inclusion bodies in skin and in brain.

Authors: B L Busard; W O Renier; F J Gabreëls; H H Jaspar; U J van Haelst; J L Slooff
Journal: Arch Neurol Date: 1986-03

4. Terminal innervation ratio in neuromuscular disease. I. Methods and controls.

Authors: C Coërs; N Telerman-Toppet; J M Gérard
Journal: Arch Neurol Date: 1973-10

5. [C2 cases of torsion spasm accompanied by chorioathetosis with numerous Lafora bodies in the external part of the globus pallidus].

Authors: J J Vanderhaeghen; J Manil; L Franken; R Cappel
Journal: Acta Neuropathol Date: 1967-08-02 Impact factor: 17.088

6. Intraneuronal polyglucosan storage restricted to the lateral pallidum (Bielschowsky bodies). A golgi, light, and electron microscopic study.

Authors: A Probst; P Sandoz; C Vanoni; J U Baumann
Journal: Acta Neuropathol Date: 1980 Impact factor: 17.088

7. Lafora disease: liver histopathology in presymptomatic children.

Authors: R J Baumann; S A Kocoshis; D Wilson
Journal: Ann Neurol Date: 1983-07 Impact factor: 10.422

8. A distinct form of adult polyglucosan body disease with massive involvement of central and peripheral neuronal processes and astrocytes: a report of four cases and a review of the occurrence of polyglucosan bodies in other conditions such as Lafora's disease and normal ageing.

Authors: Y Robitaille; S Carpenter; G Karpati; S D DiMauro
Journal: Brain Date: 1980-06 Impact factor: 13.501

9. Intraneuritic corpora amylacea. Demonstration in orbital cortex of elderly subjects by means of early postmortem brain sampling and electron microscopy.

Authors: A P Anzil; H Herrlinger; K Blinzinger; D Kronski
Journal: Virchows Arch A Pathol Anat Histol Date: 1974

Review 6. Progressive myoclonic epilepsy.

Authors: Mary L Zupanc; Benjamin Legros
Journal: Cerebellum Date: 2004 Impact factor: 3.648

6 in total

Polyglucosan bodies in intramuscular motor nerves.

1. Progressive familial myoclonic epilepsy in three families: its clinical features and pathological basis.

2. Corpora amylacea of the lumbar spinal cord and peripheral nervous system.

3. Lafora's disease. Comparison of inclusion bodies in skin and in brain.

4. Terminal innervation ratio in neuromuscular disease. I. Methods and controls.

5. [C2 cases of torsion spasm accompanied by chorioathetosis with numerous Lafora bodies in the external part of the globus pallidus].

6. Intraneuronal polyglucosan storage restricted to the lateral pallidum (Bielschowsky bodies). A golgi, light, and electron microscopic study.

7. Lafora disease: liver histopathology in presymptomatic children.

8. A distinct form of adult polyglucosan body disease with massive involvement of central and peripheral neuronal processes and astrocytes: a report of four cases and a review of the occurrence of polyglucosan bodies in other conditions such as Lafora's disease and normal ageing.

9. Intraneuritic corpora amylacea. Demonstration in orbital cortex of elderly subjects by means of early postmortem brain sampling and electron microscopy.

10. Nervous system involvement in type IV glycogenosis.

Review 1. Update on polyglucosan storage diseases.

2. Polyglucosan bodies in sural nerve biopsies.

3. Chronic demyelinating neuropathy and intra-axonal polyglucosan bodies.

4. Early detection of skin and muscular involvement in Lafora disease.

5. Uncommon types of polyglucosan bodies in the human brain: distribution and relation to disease.

Review 6. Progressive myoclonic epilepsy.