Literature DB >> 25424216

Coexistence of aplasia cutis and nevus psiloliparus--report of a novel case.

Burak Tekin1, Ayşe Deniz Yücelten, Ihsan Nuri Akpınar, Gazanfer Ekinci.   

Abstract

Nevus psiloliparus is a type of mesodermal nevus of the scalp classically seen with encephalocraniocutaneous lipomatosis. The close association between nevus psiloliparus and aplasia cutis congenita is called didymosis aplasticopsilolipara. Although typically associated with neurologic, ocular, and skeletal findings, didymosis aplasticopsilolipara can be seen without the context of encephalocraniocutaneous lipomatosis.
© 2014 Wiley Periodicals, Inc.

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Year:  2014        PMID: 25424216     DOI: 10.1111/pde.12412

Source DB:  PubMed          Journal:  Pediatr Dermatol        ISSN: 0736-8046            Impact factor:   1.588


  2 in total

1.  Encephalocraniocutaneous lipomatosis (Haberland syndrome): A mild case with bilateral cutaneous and ocular involvement.

Authors:  Jonathan Banta; Knox Beasley; Todd Kobayashi; Luis Rohena
Journal:  JAAD Case Rep       Date:  2016-04-15

2.  Encephalocraniocutaneous Lipomatosis: Haberland Syndrome.

Authors:  Selçuk Özdoğan; Ceyhun Saymaz; Cumhur Kaan Yaltırık; Hanife Gülden Düzkalır; Mustafa Kaya; Nail Demirel; Ali Haluk Düzkalır; Başar Sarıkaya; Berrin Aktekin
Journal:  Am J Case Rep       Date:  2017-12-01
  2 in total

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