Endolymphatic stromal myosis: surgical and hormonal therapy for extensive venous recurrence.

The surgical management for recurrent endolymphatic stromal myosis metastatic to the inferior vena cava is described. Positive estrogen and progesterone receptors in the resected tumor are reported. A plan of therapy is suggested for patients with endolymphatic stromal myosis, including a rationale for adjuvant progestin therapy.