Literature DB >> 25390516

Cytomegalovirus retinitis in dyskeratosis congenita.

Sara Haug1, Sandeep Randhawa, Arthur Fu, H Richard McDonald.   

Abstract

PURPOSE: The purpose of this study was to report a case of cytomegalovirus retinitis in the setting of dyskeratosis congenita.
METHODS: Case report and literature review.
RESULTS: A 23-year-old woman who had peripheral occlusive retinal vasculopathy and neovascularization as a result of pancytopenia caused by bone marrow failure also developed cytomegalovirus retinitis. She had been diagnosed with dyskeratosis congenita, which had caused the bone marrow failure and pancytopenia.
CONCLUSION: Dyskeratosis congenita is a multisystem disorder that causes bone marrow failure. It can have retinal manifestations in the form of peripheral proliferative retinopathy and retinitis.

Entities:  

Year:  2013        PMID: 25390516     DOI: 10.1097/ICB.0b013e31827aee86

Source DB:  PubMed          Journal:  Retin Cases Brief Rep        ISSN: 1935-1089


  2 in total

1.  Frosted Branch Angiitis in Pediatric Dyskeratosis Congenita: A Case Report.

Authors:  Xiao-Yu Zheng; Jia Xu; Wei Li; Si-Si Li; Cai-Ping Shi; Zheng-Yan Zhao; Jian-Hua Mao; Xi Chen
Journal:  Medicine (Baltimore)       Date:  2016-03       Impact factor: 1.889

2.  Cytomegalovirus Retinitis as a Presenting Feature of Multisystem Disorder: Dyskeratosis Congenita.

Authors:  Swapnil Parchand; Adarsh Barwad
Journal:  Middle East Afr J Ophthalmol       Date:  2017 Oct-Dec
  2 in total

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