| Literature DB >> 25332621 |
Radheshyam Purkait1, Aritra Mukherji1, Tuphan Kanti Dolai2, Ramchandra Bhadra3.
Abstract
Hemophilic pseudotumor is a rare, but well-known, complication of hemophilia occurring in 1-2 % of individuals with a severe factor VIII or IX deficiency. The hemophilic pseudotumor is defined as an encapsulated hematoma that increases of volume progressively by episodes of recurrent hemorrhage; usually originate in soft tissues or in subperiosteal or intraosseous areas. Very seldom, patient with mild form of hemophilia present with intraosseous pseudotumor. This report describe an 11-year-old boy with mild factor IX deficiency (17 % of normal factor IX activity), who developed a pseudotumor of the femur.Entities:
Keywords: Factor IX concentrates; Hemophilia B; Intraosseous pseudotumour
Year: 2014 PMID: 25332621 PMCID: PMC4192160 DOI: 10.1007/s12288-014-0414-0
Source DB: PubMed Journal: Indian J Hematol Blood Transfus ISSN: 0971-4502 Impact factor: 0.900