BACKGROUND: Dyke-Davidoff-Masson Syndrome (DDMS) is a rarely seen clinical entity which is characterised by cerebral hemiatrophy, contralateral hemiparesis and epilepsy. Radiological features are typical, such as unilateral atrophy of the cerebral hemisphere and associated compensatory bone changes in the skull, like thickening, enlargement of the paranasal sinuses and mastoid air cells. CASE REPORT: In this article, we report the first case of DDMS associated with epidermoid tumour and arachnoid cyst, who underwent operation for an epidermoid tumour in the inter-hemispheric region. To our knowledge, this is the first report of DDMS associated with multiple intracranial pathologies and this association has not been previously described in the literature. CONCLUSION: Any patient who receives DDMS in the light of clinical and radiological findings should be investigated for concomitant pathologies. Different sequences of MRI may be useful in the diagnosis of other intracranial lesions.
BACKGROUND: Dyke-Davidoff-Masson Syndrome (DDMS) is a rarely seen clinical entity which is characterised by cerebral hemiatrophy, contralateral hemiparesis and epilepsy. Radiological features are typical, such as unilateral atrophy of the cerebral hemisphere and associated compensatory bone changes in the skull, like thickening, enlargement of the paranasal sinuses and mastoid air cells. CASE REPORT: In this article, we report the first case of DDMS associated with epidermoid tumour and arachnoid cyst, who underwent operation for an epidermoid tumour in the inter-hemispheric region. To our knowledge, this is the first report of DDMS associated with multiple intracranial pathologies and this association has not been previously described in the literature. CONCLUSION: Any patient who receives DDMS in the light of clinical and radiological findings should be investigated for concomitant pathologies. Different sequences of MRI may be useful in the diagnosis of other intracranial lesions.
Authors: Dhananjaya I Bhat; B Indira Devi; A Raghunath; Sampath Somanna; B A Chandramouli Journal: Neurol India Date: 2011 Jan-Feb Impact factor: 2.117
Authors: P H Aguiar; C W Liu; H Leitão; F Issa; G Lepski; E G Figueiredo; F Gomes-Pinto; R Marino Júnior Journal: Arq Neuropsiquiatr Date: 1998-12 Impact factor: 1.420
Authors: Aslan Guzel; Mehmet Tatli; Kaya Bilguvar; Michael L Diluna; Betul Bakkaloglu; Ali K Ozturk; Fatih Bayrakli; Murat Gunel Journal: Am J Med Genet A Date: 2007-04-01 Impact factor: 2.802