Don Hayes1, Frederick R Long, Karen S McCoy, Shahid I Sheikh. Show Affiliations » 1. Department of Pediatrics, The Ohio State University College of Medicine, Columbus, Ohio, USA.
Abstract
Entities: Chemical Disease Mutation Species
Mesh: See more » Aminophenols/administration & dosageBronchiectasis/diagnostic imagingBronchiectasis/etiologyChildCystic Fibrosis/complicationsCystic Fibrosis/drug therapyCystic Fibrosis/geneticsCystic Fibrosis/physiopathologyCystic Fibrosis Transmembrane Conductance Regulator/geneticsDrug Monitoring/methodsFemaleHumansMembrane Transport Modulators/administration & dosageQuinolones/administration & dosageSpirometry/methodsTomography, X-Ray Computed/methodsTreatment Outcome
Substances: See more » AminophenolsCFTR protein, humanMembrane Transport ModulatorsQuinolonesCystic Fibrosis Transmembrane Conductance Regulatorivacaftor
Year: 2014 PMID: 25171465 DOI: 10.1159/000365999
Source DB: PubMed Journal: Respiration ISSN: 0025-7931 Impact factor: 3.580