| Literature DB >> 25127881 |
Rena C Zuo1, Daniella M Schwartz2, Chyi-Chia Richard Lee3, Milan J Anadkat4, Edward W Cowen1, Haley B Naik5.
Abstract
Key teaching points • Synovitis-acne-pustulosis-hyperostosis-osteitis (SAPHO) syndrome is characterized by distinctive osteoarticular manifestations and a spectrum of neutrophilic dermatoses. • The most common dermatologic manifestations include palmoplantar pustulosis, acne conglobata, and acne fulminans. • SAPHO syndrome should be considered in patients presenting osteoarticular pain, particularly involving the anterior chest wall and/or spine, and neutrophilic skin lesions. Published by Elsevier Inc.Entities:
Keywords: autoinflammatory; chronic recurrent multifocal osteomyelitis; neutrophilic dermatoses; palmoplantar pustulosis; synovitis-acne-pustulosis-hyperostosis-osteitis
Mesh:
Year: 2014 PMID: 25127881 PMCID: PMC4326625 DOI: 10.1016/j.jaad.2014.07.014
Source DB: PubMed Journal: J Am Acad Dermatol ISSN: 0190-9622 Impact factor: 11.527