Literature DB >> 25103454

Multiple primary (even in situ) melanomas in a patient pose significant risk to family members.

Tianhui Chen1, Kari Hemminki2, Elham Kharazmi3, Jianguang Ji4, Kristina Sundquist5, Mahdi Fallah3.   

Abstract

BACKGROUND: We aimed at assessing familial risk of melanoma by considering a detailed family history of multiple primary (invasive/in situ) melanomas (MPM), stratified by histology and location.
METHODS: Among 65,429 melanoma patients diagnosed in 1958-2010 in the Swedish Family-Cancer Database, there were 4248 patients with familial melanoma. A detailed family history of MPM was investigated by number of melanomas in one first-degree relative (FDR) and in ⩾2 FDRs. Familial melanoma risk was assessed by standardised incidence ratios (SIRs) comparing those with family history of melanoma to those without. Combining invasive/in situ melanoma was due to essentially identical familial risks.
RESULTS: For one affected FDR, familial risk increased from SIR=2.2 (95% confidence interval (CI)=2.2-2.3) for single melanoma to 16.3 (9.5-26.1) for ⩾5 melanomas, while for ⩾2 affected FDRs, the risk increased from 5.5 (4.8-6.2) for single melanoma to 23.9 (13.6-38.8) for ⩾2 melanomas. Significantly higher familial risks for superficial spreading melanoma (SSM) [2.5 (2.3-2.6)] than lentigo maligna melanoma (LMM) [1.8 (1.6-2.1)], and for multiple parts [5.3 (3.1-8.4)] and trunk [2.6 (2.5-2.8)] than head/neck [2.0 (1.8-2.2)] were observed. Only at head/neck, significantly higher risk for SSM [2.4 (1.9-3.0)] than LMM [1.6 (1.4-1.8)] was noted.
CONCLUSION: We found, for the first time, that familial risks were similar for two/three melanomas in one FDR or for a single melanoma in ⩾2 FDRs and, higher familial risks for SSM than LMM occurred only at head/neck. This study provides new evidence for genetic counselling in melanoma, suggesting the need for considering not only the number of affected family members but also the diagnosis of MPM (even in situ) in relatives.
Copyright © 2014 Elsevier Ltd. All rights reserved.

Entities:  

Keywords:  Age at diagnosis; Familial risk; Family history; First-degree relatives; Histology; Melanoma; Multiple primary melanomas

Mesh:

Year:  2014        PMID: 25103454     DOI: 10.1016/j.ejca.2014.07.007

Source DB:  PubMed          Journal:  Eur J Cancer        ISSN: 0959-8049            Impact factor:   9.162


  12 in total

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Authors:  Jazlyn Read; Judith Symmons; Jane M Palmer; Grant W Montgomery; Nicholas G Martin; Nicholas K Hayward
Journal:  Fam Cancer       Date:  2016-10       Impact factor: 2.375

2.  Improvement of Genetic Testing for Cutaneous Melanoma in Countries With Low to Moderate Incidence: The Rule of 2 vs the Rule of 3.

Authors:  Juliette Delaunay; Ludovic Martin; Brigitte Bressac-de Paillerets; Gerard Duru; Olivier Ingster; Luc Thomas
Journal:  JAMA Dermatol       Date:  2017-11-01       Impact factor: 10.282

3.  Frequency and characteristics of familial melanoma in Spain: the FAM-GEM-1 Study.

Authors:  Iván Márquez-Rodas; Manuel Martín González; Eduardo Nagore; Cristina Gómez-Fernández; Jose Antonio Avilés-Izquierdo; Cayetana Maldonado-Seral; Virtudes Soriano; Margarita Majem-Tarruella; Virginia Palomar; Rocio Maseda; Alfonso Martín-Carnicero; Teresa Puertolas; Elena Godoy; Pablo Cerezuela; Maria Ochoa de Olza; Begoña Campos; Elisabeth Perez-Ruiz; Ainara Soria; Irene Gil-Arnaiz; Maria Gonzalez-Cao; Elisa Galvez; Ana Arance; Joaquin Belon; Luis de la Cruz-Merino; Salvador Martín-Algarra
Journal:  PLoS One       Date:  2015-04-13       Impact factor: 3.240

4.  Risk of other Cancers in Families with Melanoma: Novel Familial Links.

Authors:  Christoph Frank; Jan Sundquist; Akseli Hemminki; Kari Hemminki
Journal:  Sci Rep       Date:  2017-02-15       Impact factor: 4.379

5.  Second primary cancer after female breast cancer: Familial risks and cause of death.

Authors:  Guoqiao Zheng; Akseli Hemminki; Asta Försti; Jan Sundquist; Kristina Sundquist; Kari Hemminki
Journal:  Cancer Med       Date:  2018-11-26       Impact factor: 4.452

6.  Familial Risks and Mortality in Second Primary Cancers in Melanoma.

Authors:  Subhayan Chattopadhyay; Akseli Hemminki; Asta Försti; Kristina Sundquist; Jan Sundquist; Kari Hemminki
Journal:  JNCI Cancer Spectr       Date:  2019-01-09

7.  Comparison of Familial Clustering of Anogenital and Skin Cancers Between In Situ and Invasive Types.

Authors:  Luyao Zhang; Otto Hemminki; Guoqiao Zheng; Asta Försti; Kristina Sundquist; Jan Sundquist; Kari Hemminki
Journal:  Sci Rep       Date:  2019-11-06       Impact factor: 4.379

8.  Eleven Primary Melanomas, Colon Cancer, and Atypical Nevi in the Same Patient: A Case Report and Literature Review.

Authors:  Lea Juul Nielsen; Lisbet Rosenkrantz Hölmich
Journal:  Case Rep Dermatol Med       Date:  2016-02-28

9.  Prostate cancer survivors: Risk and mortality in second primary cancers.

Authors:  Subhayan Chattopadhyay; Guoqiao Zheng; Otto Hemminki; Asta Försti; Kristina Sundquist; Kari Hemminki
Journal:  Cancer Med       Date:  2018-10-01       Impact factor: 4.452

10.  Second Primary Cancers in Melanoma Patients Critically Shorten Survival.

Authors:  Guoqiao Zheng; Subhayan Chattopadhyay; Kristina Sundquist; Jan Sundquist; Asta Försti; Akseli Hemminki; Kari Hemminki
Journal:  Clin Epidemiol       Date:  2020-01-23       Impact factor: 4.790

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