S B Cehreli1, R B Brannon2, R J Musselman3, R E Tirali1, M Derbent4. 1. Başkent University Faculty of Dentistry, Paediatric Dentistry, Bağl?ca, Turkey. 2. Deceased, Former Head Louisiana State University Health Sciences Center. 3. Louisiana State University Health Sciences Center, School of Dentistry, Department of Pediatric Dentistry. 4. Başkent University Faculty of Medicine, Department of Paediatrics, Bağl?ca, Turkey.
Abstract
BACKGROUND: Otodental syndrome is a rare condition characterised by globodontia, and sensorineural high frequency hearing loss. To date, only 20 cases of otodental syndrome have been reported. CASE REPORT: A 6 year-old girl presented with a chief complaint of delay in the eruption of primary canines. Following clinical, radiographic and audiologic evaluations, the patient was diagnosed with otodental syndrome. CONCLUSION: Globodontia is a diagnostic feature of the otodental syndrome, which often provides the path to discovery of the associated hearing loss. Missing teeth, arch-size discrepancies, chewing problems and teething disturbances are the other major complications.
BACKGROUND:Otodental syndrome is a rare condition characterised by globodontia, and sensorineural high frequency hearing loss. To date, only 20 cases of otodental syndrome have been reported. CASE REPORT: A 6 year-old girl presented with a chief complaint of delay in the eruption of primary canines. Following clinical, radiographic and audiologic evaluations, the patient was diagnosed with otodental syndrome. CONCLUSION: Globodontia is a diagnostic feature of the otodental syndrome, which often provides the path to discovery of the associated hearing loss. Missing teeth, arch-size discrepancies, chewing problems and teething disturbances are the other major complications.