Literature DB >> 25022704

Glycosaminoglycans can be associated with oxidative damage in mucopolysaccharidosis II patients submitted to enzyme replacement therapy.

G W Negretto1, M Deon, G B Biancini, M G Burin, R Giugliani, C R Vargas.   

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Year:  2014        PMID: 25022704     DOI: 10.1007/s10565-014-9284-3

Source DB:  PubMed          Journal:  Cell Biol Toxicol        ISSN: 0742-2091            Impact factor:   6.691


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  4 in total

1.  Evaluation of oxidative stress and mitochondrial function in a type II mucopolysaccharidosis cellular model: in vitro effects of genistein and coenzyme Q10.

Authors:  Carlos Eduardo Diaz Jacques; Franciele Fátima Lopes; Edina Poletto; Luisa Natalia Pimentel Vera; Priscila Vianna; Luiza Steffens Reinhardt; Guilherme Baldo; Carmen Regla Vargas
Journal:  Metab Brain Dis       Date:  2022-08-27       Impact factor: 3.655

2.  Human kidney organoids reveal the role of glutathione in Fabry disease.

Authors:  Jin Won Kim; Hyung Wook Kim; Sun Ah Nam; Jong Young Lee; Hae Jin Cho; Tae-Min Kim; Yong Kyun Kim
Journal:  Exp Mol Med       Date:  2021-10-15       Impact factor: 8.718

Review 3.  The pathophysiological role of mitochondrial oxidative stress in lung diseases.

Authors:  Xiaojing Liu; Zhihong Chen
Journal:  J Transl Med       Date:  2017-10-13       Impact factor: 5.531

Review 4.  Diagnosis of Mucopolysaccharidoses.

Authors:  Francyne Kubaski; Fabiano de Oliveira Poswar; Kristiane Michelin-Tirelli; Maira Graeff Burin; Diana Rojas-Málaga; Ana Carolina Brusius-Facchin; Sandra Leistner-Segal; Roberto Giugliani
Journal:  Diagnostics (Basel)       Date:  2020-03-22
  4 in total

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