| Literature DB >> 24925197 |
Christopher K Bichakjian1, Thomas Olencki1, Murad Alam1, James S Andersen1, Daniel Berg1, Glen M Bowen1, Richard T Cheney1, Gregory A Daniels1, L Frank Glass1, Roy C Grekin1, Kenneth Grossman1, Alan L Ho1, Karl D Lewis1, Daniel D Lydiatt1, William H Morrison1, Kishwer S Nehal1, Kelly C Nelson1, Paul Nghiem1, Clifford S Perlis1, Ashok R Shaha1, Wade L Thorstad1, Malika Tuli1, Marshall M Urist1, Timothy S Wang1, Andrew E Werchniak1, Sandra L Wong1, John A Zic1, Nicole McMillian1, Karin Hoffman1, Maria Ho1.
Abstract
Dermatofibrosarcoma protuberans (DFSP) is an uncommon soft tissue tumor characterized by a relatively high risk of local recurrence and low risk of metastasis. The NCCN Guidelines for DFSP provide multidisciplinary recommendations on the management of patients with this rare disease. These NCCN Guidelines Insights highlight the addition of the Principles of Pathology section, which provides recommendations on the pathologic assessment of DFSP. Because DFSP can mimic other lesions, immunohistochemical studies are often required to establish diagnosis. Cytogenetic testing for the characteristic translocation t(17;22)(q22;q13) can also be valuable in the differential diagnosis of DFSP with other histologically similar tumors.Entities:
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Year: 2014 PMID： 24925197 DOI： 10.6004/jnccn.2014.0081
Source DB: PubMed Journal: J Natl Compr Canc Netw ISSN： 1540-1405 Impact factor: 11.908