Sevinc Sarinc Ulasli1, Elif Kupeli2. 1. Department of Pulmonary Diseases, Faculty of Medicine, Afyon Kocatepe University, Afyon, Turkey. 2. Department of Pulmonary Diseases, Faculty of Medicine, Baskent University, Ankara, Turkey.
Abstract
BACKGROUND: Tracheobronchopathia osteochondroplastica (TBPOCP) is an uncommon benign condition affecting the lumen of tracheobronchial tree and characterized by abnormal chondrification and ossification. TBPOCP is more frequent than it has been reported, as it can be asymptomatic or present with non-specific respiratory symptoms. AIMS: In this article, we provide a review of the English literature on the condition and discuss its clinical features, general principles, diagnostic approaches and current treatment recommendations for TBPOCP. METHODS: We searched for all papers indexed in Science Citation Index and Science Citation Index - Expanded by using Thomson Reuters Web of Knowledge Web of Science software. RESULTS: We reviewed a total of 72 scientific publications. CONCLUSION: In order to highlight, diagnosis, treatment and treatment outcomes of TBPOCP, further review articles and large case series about this orphan disease are needed.
BACKGROUND:Tracheobronchopathia osteochondroplastica (TBPOCP) is an uncommon benign condition affecting the lumen of tracheobronchial tree and characterized by abnormal chondrification and ossification. TBPOCP is more frequent than it has been reported, as it can be asymptomatic or present with non-specific respiratory symptoms. AIMS: In this article, we provide a review of the English literature on the condition and discuss its clinical features, general principles, diagnostic approaches and current treatment recommendations for TBPOCP. METHODS: We searched for all papers indexed in Science Citation Index and Science Citation Index - Expanded by using Thomson Reuters Web of Knowledge Web of Science software. RESULTS: We reviewed a total of 72 scientific publications. CONCLUSION: In order to highlight, diagnosis, treatment and treatment outcomes of TBPOCP, further review articles and large case series about this orphan disease are needed.
Authors: Alessandro G Fois; Antonella Arcadu; Luigi Santoru; Rocco Trisolini; Vincenzo Marras; Giorgio C Ginesu; Sara Canu; Lorenzo Cordero; Gabriella Diana; Pietro Pirina Journal: Multidiscip Respir Med Date: 2016-04-19