Literature DB >> 24844137

Clinical investigational studies for validation of a next-generation sequencing in vitro diagnostic device for cystic fibrosis testing.

Daniel S Grosu1, Lynda Hague, Manjula Chelliserry, Kristina M Kruglyak, Ross Lenta, Brandy Klotzle, Jonathan San, Wendy M Goldstein, Sharmili Moturi, Patricia Devers, Julie Woolworth, Eric Peters, Barbara Elashoff, Jay Stoerker, Daynna J Wolff, Kenneth J Friedman, W Edward Highsmith, Erick Lin, Frank S Ong.   

Abstract

PURPOSE: Clinical investigational studies were conducted to demonstrate the accuracy and reproducibility of the Illumina MiSeqDx CF System, a next-generation sequencing (NGS) in vitro diagnostic device for cystic fibrosis testing.
METHODS: Two NGS assays - a Clinical Sequencing Assay (Sequencing Assay) and a 139-Variant Assay (Variant Assay) - were evaluated in both an Accuracy Study and a Reproducibility Study, with comparison to bi-directional Sanger sequencing and PCR as reference methods. For each study, positive agreement (PA), negative agreement (NA), and overall agreement (OA) were evaluated.
RESULTS: In the Accuracy Study, the Sequencing Assay achieved PA of 99.7% including the polyTG/polyT region and PA of 100% excluding the region. The Variant Assay achieved PA of 100%. NA and OA were >99.99% for both Assays. In the Reproducibility Study, the Sequencing Assay achieved PA of 99.2%; NA and OA were both 99.7%. The Variant Assay achieved PA of 99.8%; NA and OA were both 99.9%. Sample pass rates were 99.7% in both studies for both assays.
CONCLUSION: This is the first systematic evaluation of a NGS platform for broad clinical use as an in vitro diagnostic, including accuracy validation with multiple reference methods and reproducibility validation at multiple clinical sites. These NGS-based Assays had accurate and reproducible results which were comparable to or better than other methods currently in clinical use for clinical genetic testing of cystic fibrosis.

Entities:  

Keywords:  clinical validation; cystic fibrosis; in vitro diagnostics; next-generation sequencing; sequencing-by-synthesis

Mesh:

Year:  2014        PMID: 24844137     DOI: 10.1586/14737159.2014.916618

Source DB:  PubMed          Journal:  Expert Rev Mol Diagn        ISSN: 1473-7159            Impact factor:   5.225


  8 in total

Review 1.  Personalized and precision medicine: integrating genomics into treatment decisions in gastrointestinal malignancies.

Authors:  Trang H Au; Kai Wang; David Stenehjem; Ignacio Garrido-Laguna
Journal:  J Gastrointest Oncol       Date:  2017-06

2.  A Novel Pathogenic Variant of the CFTR Gene in a Patient with Cystic Fibrosis Phenotype-c.4096A > T.

Authors:  Ahmet Burak Arslan; Ayşe Gül Zamani; Sevgi Pekcan; Mahmut Selman Yıldırım
Journal:  J Pediatr Genet       Date:  2019-08-28

3.  Next-Generation Molecular Testing of Newborn Dried Blood Spots for Cystic Fibrosis.

Authors:  Martina I Lefterova; Peidong Shen; Justin I Odegaard; Eula Fung; Tsoyu Chiang; Gang Peng; Ronald W Davis; Wenyi Wang; Martin Kharrazi; Iris Schrijver; Curt Scharfe
Journal:  J Mol Diagn       Date:  2016-02-01       Impact factor: 5.568

4.  Novel findings with reassessment of exome data: implications for validation testing and interpretation of genomic data.

Authors:  Kristin McDonald Gibson; Addie Nesbitt; Kajia Cao; Zhenming Yu; Elizabeth Denenberg; Elizabeth DeChene; Qiaoning Guan; Elizabeth Bhoj; Xiangdong Zhou; Bo Zhang; Chao Wu; Holly Dubbs; Alisha Wilkens; Livija Medne; Emma Bedoukian; Peter S White; Jeffrey Pennington; Minjie Luo; Laura Conlin; Dimitri Monos; Mahdi Sarmady; Eric Marsh; Elaine Zackai; Nancy Spinner; Ian Krantz; Matt Deardorff; Avni Santani
Journal:  Genet Med       Date:  2017-10-12       Impact factor: 8.822

5.  Validation of a semiconductor next-generation sequencing assay for the clinical genetic screening of CFTR.

Authors:  Daniel Trujillano; Maximilian E R Weiss; Julia Köster; Efstathios B Papachristos; Martin Werber; Krishna Kumar Kandaswamy; Anett Marais; Sabrina Eichler; Jenny Creed; Erol Baysal; Iqbal Yousuf Jaber; Dina Ahmed Mehaney; Chantal Farra; Arndt Rolfs
Journal:  Mol Genet Genomic Med       Date:  2015-04-16       Impact factor: 2.183

6.  The Role of Next-Generation Sequencing in Enabling Personalized Oncology Therapy.

Authors:  C A Cummings; E Peters; L Lacroix; F Andre; M R Lackner
Journal:  Clin Transl Sci       Date:  2016-11-15       Impact factor: 4.689

7.  Cystic fibrosis newborn screening programs: implications of the CFTR variant spectrum in nonwhite patients.

Authors:  Lynn Pique; Steve Graham; Michelle Pearl; Martin Kharrazi; Iris Schrijver
Journal:  Genet Med       Date:  2016-05-05       Impact factor: 8.822

Review 8.  Ultra-rare Disease and Genomics-Driven Precision Medicine.

Authors:  Sangmoon Lee; Murim Choi
Journal:  Genomics Inform       Date:  2016-06-30
  8 in total

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