Literature DB >> 24816438

Transfusion therapy and alloimmunization in Thalassemia Intermedia: a 10 year experience at a tertiary care university hospital.

Arwa Z Al-Riyami1, Sabah Al-Mahrooqi1, Sumaiya Al-Hinai1, Saif Al-Hosni1, Ali Al-Madhani2, Shahina Daar3.   

Abstract

BACKGROUND: Thalassemia Intermedia (TI) has a wide clinical profile with many patients requiring only occasional transfusions. To prevent alloimmunization, we adopted a policy of issuing phenotype matched red blood cells in 2009. We examined transfusion indications and alloimmunization rate in TI patients. STUDY DESIGN AND METHODS: Clinical and blood bank records of 37 TI patients were reviewed.
RESULTS: 23 Patients required transfusion for pregnancy (26), splenectomy (8) and anemia (11). Since 2009, total of 335 units were transfused with only one antibody developing after transfusing a non-phenotype matched unit.
CONCLUSION: The commonest indication for blood transfusion was pregnancy. Providing phenotype matched blood has successfully reduced the rate of alloimmunization.
Copyright © 2014 Elsevier Ltd. All rights reserved.

Entities:  

Keywords:  Alloimmunization; Phenotype; Thalassemia Intermedia; Transfusion

Mesh:

Year:  2014        PMID: 24816438     DOI: 10.1016/j.transci.2014.04.009

Source DB:  PubMed          Journal:  Transfus Apher Sci        ISSN: 1473-0502            Impact factor:   1.764


  4 in total

1.  Red blood cell alloimmunisation in transfusion-dependent thalassaemia: a systematic review.

Authors:  Massimo Franchini; Gian Luca Forni; Giuseppe Marano; Mario Cruciani; Carlo Mengoli; Valeria Pinto; Lucia De Franceschi; Donatella Venturelli; Maddalena Casale; Martina Amerini; Martina Capuzzo; Giuliano Grazzini; Francesca Masiello; Ilaria Pati; Eva Veropalumbo; Stefania Vaglio; Simonetta Pupella; Giancarlo M Liumbruno
Journal:  Blood Transfus       Date:  2019-01       Impact factor: 3.443

Review 2.  Transfusion in Haemoglobinopathies: Review and recommendations for local blood banks and transfusion services in Oman.

Authors:  Arwa Z Al-Riyami; Shahina Daar
Journal:  Sultan Qaboos Univ Med J       Date:  2018-04-04

3.  Prevalence of Red Blood Cell Major Blood Group Antigens and Phenotypes among Omani Blood Donors.

Authors:  Arwa Z Al-Riyami; Ali Al-Marhoobi; Saif Al-Hosni; Sabah Al Mahrooqi; Michael Schmidt; Sheila O'Brien; Murtadha Al-Khabori
Journal:  Oman Med J       Date:  2019-11

Review 4.  When to consider transfusion therapy for patients with non-transfusion-dependent thalassaemia.

Authors:  A T Taher; A Radwan; V Viprakasit
Journal:  Vox Sang       Date:  2014-10-07       Impact factor: 2.144

  4 in total

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