Literature DB >> 24768253

Obliterative portal venopathy: a study of 48 children.

Stéphanie Franchi-Abella1, Monique Fabre2, Emmanuel Mselati3, Marise Elia De Marsillac4, Mohamed Bayari4, Danièle Pariente1, Emmanuel Jacquemin5, Olivier Bernard6.   

Abstract

Childhood obliterative portal venopathy presents at any age and may be genetic in origin. We report 48 children with obliterative portal venopathy, based on strict histologic criteria, investigated between 1972 and 2011. Diagnosis requires histology and is suggested by ultrasonography findings. Portal hypertension is the main complication but is absent in some cases. Prognosis is relatively good, but the detection of cardiopulmonary complications is essential.
Copyright © 2014 Elsevier Inc. All rights reserved.

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Year:  2014        PMID: 24768253     DOI: 10.1016/j.jpeds.2014.03.025

Source DB:  PubMed          Journal:  J Pediatr        ISSN: 0022-3476            Impact factor:   4.406


  11 in total

1.  Pediatric non-cirrhotic portal fibrosis: role of endoscopic management in determining long-term outcome.

Authors:  Durga Prasad; Moinak Sen Sarma; Surender Kumar Yachha; Anshu Srivastava; Ujjal Poddar
Journal:  Hepatol Int       Date:  2019-08-29       Impact factor: 6.047

Review 2.  Pathology of idiopathic non-cirrhotic portal hypertension.

Authors:  Maria Guido; Samantha Sarcognato; Diana Sacchi; Guido Colloredo
Journal:  Virchows Arch       Date:  2018-04-12       Impact factor: 4.064

Review 3.  Idiopathic portal hypertension and extrahepatic portal venous obstruction.

Authors:  Rajeev Khanna; Shiv Kumar Sarin
Journal:  Hepatol Int       Date:  2018-02-20       Impact factor: 6.047

Review 4.  Hepatocellular nodules in vascular liver diseases.

Authors:  Christine Sempoux; Charles Balabaud; Valérie Paradis; Paulette Bioulac-Sage
Journal:  Virchows Arch       Date:  2018-05-26       Impact factor: 4.064

Review 5.  Multimodality imaging of obliterative portal venopathy: what every radiologist should know.

Authors:  A Arora; S K Sarin
Journal:  Br J Radiol       Date:  2014-12-16       Impact factor: 3.039

6.  Haploinsufficiency of the NOTCH1 Receptor as a Cause of Adams-Oliver Syndrome With Variable Cardiac Anomalies.

Authors:  Rajiv D Machado; Richard C Trembath; Laura Southgate; Maja Sukalo; Anastasios S V Karountzos; Edward J Taylor; Claire S Collinson; Deborah Ruddy; Katie M Snape; Bruno Dallapiccola; John L Tolmie; Shelagh Joss; Francesco Brancati; M Cristina Digilio; Luitgard M Graul-Neumann; Leonardo Salviati; Wiltrud Coerdt; Emmanuel Jacquemin; Wim Wuyts; Martin Zenker
Journal:  Circ Cardiovasc Genet       Date:  2015-05-11

Review 7.  Idiopathic Non-Cirrhotic Portal Hypertension and Porto-Sinusoidal Vascular Disease: Review of Current Data.

Authors:  Michel Kmeid; Xiuli Liu; Samuel Ballentine; Hwajeong Lee
Journal:  Gastroenterology Res       Date:  2021-04-21

Review 8.  Idiopathic non-cirrhotic portal hypertension: a review.

Authors:  Jeoffrey N L Schouten; Joanne Verheij; Susana Seijo
Journal:  Orphanet J Rare Dis       Date:  2015-05-30       Impact factor: 4.123

Review 9.  Diagnostic challenges in non-cirrhotic portal hypertension - porto sinusoidal vascular disease.

Authors:  Oana Nicoară-Farcău; Ioana Rusu; Horia Stefănescu; Marcel Tanțău; Radu Ion Badea; Bogdan Procopeț
Journal:  World J Gastroenterol       Date:  2020-06-14       Impact factor: 5.742

Review 10.  Idiopathic Noncirrhotic Portal Hypertension: An Appraisal.

Authors:  Hwajeong Lee; Aseeb Ur Rehman; M Isabel Fiel
Journal:  J Pathol Transl Med       Date:  2015-11-11
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