Literature DB >> 24687702

Primary ciliary dyskinesia and cystic fibrosis: different diseases require different treatment.

Jane S Lucas1, Mary Carroll2.   

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Year:  2014        PMID: 24687702     DOI: 10.1378/chest.13-2590

Source DB:  PubMed          Journal:  Chest        ISSN: 0012-3692            Impact factor:   9.410


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  11 in total

1.  A quality-of-life measure for adults with primary ciliary dyskinesia: QOL-PCD.

Authors:  Jane S Lucas; Laura Behan; Audrey Dunn Galvin; Adrianne Alpern; Anjana M Morris; Mary P Carroll; Michael R Knowles; Margaret W Leigh; Alexandra L Quittner
Journal:  Eur Respir J       Date:  2015-05-14       Impact factor: 16.671

2.  Validation of a health-related quality of life instrument for primary ciliary dyskinesia (QOL-PCD).

Authors:  Laura Behan; Margaret W Leigh; Sharon D Dell; Audrey Dunn Galvin; Alexandra L Quittner; Jane S Lucas
Journal:  Thorax       Date:  2017-02-28       Impact factor: 9.139

3.  Proceedings of the COST action BM1407 inaugural conference BEAT-PCD: translational research in primary ciliary dyskinesia - bench, bedside, and population perspectives.

Authors:  Bruna Rubbo; Laura Behan; Eleonora Dehlink; Myrofora Goutaki; Claire Hogg; Panayiotis Kouis; Claudia E Kuehni; Philipp Latzin; Kim Nielsen; Dominic Norris; Sylvia Nyilas; Mareike Price; Jane S Lucas
Journal:  BMC Proc       Date:  2016-11-29

4.  Pulmonary exacerbations in patients with primary ciliary dyskinesia: an expert consensus definition for use in clinical trials.

Authors:  Jane S Lucas; Florian Gahleitner; Adelina Amorim; Mieke Boon; Philippa Brown; Carolina Constant; Simon Cook; Suzanne Crowley; Damien M S Destouches; Ernst Eber; Huda Mussaffi; Eric Haarman; Amanda Harris; Cordula Koerner-Rettberg; Claudia E Kuehni; Philipp Latzin; Michael R Loebinger; Natalie Lorent; Bernard Maitre; Antonio Moreno-Galdó; Kim G Nielsen; Uğur Özçelik; Lue Katrine Drasbæk Philipsen; Petr Pohunek; Eva Polverino; Jessica Rademacher; Phil Robinson; Deborah Snijders; Panayiotis Yiallouros; Siobhán B Carr
Journal:  ERJ Open Res       Date:  2019-02-01

Review 5.  Lower airway clinical outcome measures for use in primary ciliary dyskinesia research: a scoping review.

Authors:  Florian Gahleitner; James Thompson; Claire L Jackson; Jana F Hueppe; Laura Behan; Eleonora Dehlink; Myrofora Goutaki; Florian Halbeisen; Ana Paula L Queiroz; Guillaume Thouvenin; Claudia E Kuehni; Philipp Latzin; Jane S Lucas; Bruna Rubbo
Journal:  ERJ Open Res       Date:  2021-11-29

6.  Genetics, diagnosis, and future treatment strategies for primary ciliary dyskinesia.

Authors:  M Leigh Anne Daniels; Peadar G Noone
Journal:  Expert Opin Orphan Drugs       Date:  2014-11-29       Impact factor: 0.694

Review 7.  Diagnosis and management of primary ciliary dyskinesia.

Authors:  Jane S Lucas; Andrea Burgess; Hannah M Mitchison; Eduardo Moya; Michael Williamson; Claire Hogg
Journal:  Arch Dis Child       Date:  2014-04-25       Impact factor: 3.791

Review 8.  Diagnosis, monitoring, and treatment of primary ciliary dyskinesia: PCD foundation consensus recommendations based on state of the art review.

Authors:  Adam J Shapiro; Maimoona A Zariwala; Thomas Ferkol; Stephanie D Davis; Scott D Sagel; Sharon D Dell; Margaret Rosenfeld; Kenneth N Olivier; Carlos Milla; Sam J Daniel; Adam J Kimple; Michele Manion; Michael R Knowles; Margaret W Leigh
Journal:  Pediatr Pulmonol       Date:  2015-09-29

9.  Proceedings of the 2nd BEAT-PCD conference and 3rd PCD training school: part 1.

Authors:  Florian Halbeisen; Claire Hogg; Mikkel C Alanin; Zuzanna Bukowy-Bieryllo; Francisco Dasi; Julie Duncan; Amanda Friend; Myrofora Goutaki; Claire Jackson; Victoria Keenan; Amanda Harris; Robert A Hirst; Philipp Latzin; Gemma Marsh; Kim Nielsen; Dominic Norris; Daniel Pellicer; Ana Reula; Bruna Rubbo; Nisreen Rumman; Amelia Shoemark; Woolf T Walker; Claudia E Kuehni; Jane S Lucas
Journal:  BMC Proc       Date:  2018-03-05

10.  Modelling of primary ciliary dyskinesia using patient-derived airway organoids.

Authors:  Jelte van der Vaart; Lena Böttinger; Maarten H Geurts; Willine J van de Wetering; Kèvin Knoops; Norman Sachs; Harry Begthel; Jeroen Korving; Carmen Lopez-Iglesias; Peter J Peters; Kerem Eitan; Alex Gileles-Hillel; Hans Clevers
Journal:  EMBO Rep       Date:  2021-10-25       Impact factor: 8.807

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