Hyun Woo Goo1, Sang-Hyub Park, Hyun Jung Koo, Young Hoon Cho, Eunsol Lee. 1. Department of Radiology and Research Institute of Radiology, University of Ulsan College of Medicine, Asan Medical Center, 88 Olympic-ro 43-gil, Songpa-gu, Seoul, 138-736, Republic of Korea, hwgoo@amc.seoul.kr.
Abstract
BACKGROUND: Imaging findings of bilateral pulmonary vein atresia have not been described. OBJECTIVE: To describe cardiac CT findings and clinical outcomes of bilateral pulmonary vein atresia. MATERIALS AND METHODS: Three newborns with bilateral pulmonary vein atresia were encountered at our institution during a period of 8 years. We evaluated prenatal echocardiographic findings, clinical presentations, postnatal echocardiographic findings, chest radiographic findings, cardiac CT findings and clinical outcomes. RESULTS: All newborns presented immediately after birth with severe cyanosis, respiratory distress and acidosis that were unresponsive to medical management. Prenatal and postnatal echocardiographic studies and chest radiography were misleading, inconclusive or nonspecific in making the diagnosis in these children; however cardiac CT clearly demonstrated atresia of the bilateral pulmonary veins with multiple small mediastinal collateral veins and pulmonary edema. Surgical treatments were not feasible for this anomaly. Their clinical outcomes were universally dismal and all infants died within 3 days. CONCLUSION: Cardiac CT provides an accurate diagnosis of bilateral pulmonary vein atresia and leads to prompt treatment decision in these children.
BACKGROUND: Imaging findings of bilateral pulmonary vein atresia have not been described. OBJECTIVE: To describe cardiac CT findings and clinical outcomes of bilateral pulmonary vein atresia. MATERIALS AND METHODS: Three newborns with bilateral pulmonary vein atresia were encountered at our institution during a period of 8 years. We evaluated prenatal echocardiographic findings, clinical presentations, postnatal echocardiographic findings, chest radiographic findings, cardiac CT findings and clinical outcomes. RESULTS: All newborns presented immediately after birth with severe cyanosis, respiratory distress and acidosis that were unresponsive to medical management. Prenatal and postnatal echocardiographic studies and chest radiography were misleading, inconclusive or nonspecific in making the diagnosis in these children; however cardiac CT clearly demonstrated atresia of the bilateral pulmonary veins with multiple small mediastinal collateral veins and pulmonary edema. Surgical treatments were not feasible for this anomaly. Their clinical outcomes were universally dismal and all infants died within 3 days. CONCLUSION: Cardiac CT provides an accurate diagnosis of bilateral pulmonary vein atresia and leads to prompt treatment decision in these children.
Authors: K K Pourmoghadam; J W Moore; M Khan; E M Geary; N Madan; B J Wolfson; J P de Chadarevian; D S Holsclaw; M L Jacobs Journal: Pediatr Cardiol Date: 2002-09-25 Impact factor: 1.655
Authors: Peter K T Hui; Hyun Woo Goo; Jing Du; Janice J K Ip; Suzu Kanzaki; Young Jin Kim; Supika Kritsaneepaiboon; Oktavia Lilyasari; Suvipaporn Siripornpitak Journal: Pediatr Radiol Date: 2017-04-24
Authors: Martin Ngie Liong Wong; Ing Ping Tang; Yek Kee Chor; Kiew Siong Lau; Anne Rachel John; King Ching Hii; Olive Pei Yi Lee; Wooi Kok Lim; Hannah Pei Koon Tan Journal: BMC Pediatr Date: 2020-09-24 Impact factor: 2.125