| Literature DB >> 24533415 |
S Raghunandhan1, P Vijaya Krishnan1, Sathiya Murali1, R S Anand Kumar1, Mohan Kameswaran1.
Abstract
Patients with intractable vertigo often present a diagnostic dilemma to the treating physician. A wide spectrum of diseases, ranging from those of the labyrinth onto the central nervous system, may present predominantly with vertigo. In some cases, it requires the clinical acumen of an experienced neuro-otologist, to decipher these vertiginous symptoms and arrive at a definitive diagnosis. Meniere's syndrome is one such phenomenon, where the endolymphatic hydrops may be attributable to varied aetiology. We report a case of sporadic (non-syndromic) Endolymphatic Sac Tumor which presented to us, mimicking a classical Meniere's syndrome. We discuss its clinical presentation, diagnostic modalities, operative technique and histo-pathological features. The case is reported along with a review of the world literature on this tumor, highlighting the diagnostic and management protocols advocated for this rare entity. Endolymphatic sac tumor is a rare entity which may masquerade as a classical case of Meniere's syndrome, wherein the triad of symptoms (as in endolymphatic hydrops) may not be alleviated by the usual treatment protocols. Tracing the aetiology of these symptoms, remains the most crucial factor in treating such patients.Entities:
Keywords: Endolymphatic hydrops; Endolymphatic sac tumor (ELST); Vertigo; Von Hippel–Lindau’s disease (VHL)
Year: 2011 PMID: 24533415 PMCID: PMC3918290 DOI: 10.1007/s12070-011-0395-3
Source DB: PubMed Journal: Indian J Otolaryngol Head Neck Surg ISSN: 2231-3796