Literature DB >> 24533415

Endolymphatic Sac Tumour: A Neoplastic Cause for Meniere's Syndrome.

S Raghunandhan1, P Vijaya Krishnan1, Sathiya Murali1, R S Anand Kumar1, Mohan Kameswaran1.   

Abstract

Patients with intractable vertigo often present a diagnostic dilemma to the treating physician. A wide spectrum of diseases, ranging from those of the labyrinth onto the central nervous system, may present predominantly with vertigo. In some cases, it requires the clinical acumen of an experienced neuro-otologist, to decipher these vertiginous symptoms and arrive at a definitive diagnosis. Meniere's syndrome is one such phenomenon, where the endolymphatic hydrops may be attributable to varied aetiology. We report a case of sporadic (non-syndromic) Endolymphatic Sac Tumor which presented to us, mimicking a classical Meniere's syndrome. We discuss its clinical presentation, diagnostic modalities, operative technique and histo-pathological features. The case is reported along with a review of the world literature on this tumor, highlighting the diagnostic and management protocols advocated for this rare entity. Endolymphatic sac tumor is a rare entity which may masquerade as a classical case of Meniere's syndrome, wherein the triad of symptoms (as in endolymphatic hydrops) may not be alleviated by the usual treatment protocols. Tracing the aetiology of these symptoms, remains the most crucial factor in treating such patients.

Entities:  

Keywords:  Endolymphatic hydrops; Endolymphatic sac tumor (ELST); Vertigo; Von Hippel–Lindau’s disease (VHL)

Year:  2011        PMID: 24533415      PMCID: PMC3918290          DOI: 10.1007/s12070-011-0395-3

Source DB:  PubMed          Journal:  Indian J Otolaryngol Head Neck Surg        ISSN: 2231-3796


  15 in total

Review 1.  Endolymphatic sac tumor: a case report and review of the literature.

Authors:  J Reijneveld; P Hanlo; G Groenewoud; G Jansen; K van Overbeeke; C Tulleken
Journal:  Surg Neurol       Date:  1997-10

2.  Endolymphatic sac tumor in a patient with von Hippel-Lindau disease: MR imaging findings.

Authors:  Ozgür Kiliçkesmez
Journal:  Diagn Interv Radiol       Date:  2006-03       Impact factor: 2.630

3.  Endolymphatic sac tumour: a rare cause of recurrent vertigo.

Authors:  Y K Ong; N W C Chee; P Y K Hwang; J Goh
Journal:  Singapore Med J       Date:  2006-07       Impact factor: 1.858

4.  von Hippel-Lindau disease gene alterations associated with endolymphatic sac tumor.

Authors:  A O Vortmeyer; D Choo; S D Pack; E Oldfield; Z Zhuang
Journal:  J Natl Cancer Inst       Date:  1997-07-02       Impact factor: 13.506

5.  Endolymphatic sac tumours: surgical management.

Authors:  Jörg Schipper; Wolfgang Maier; Steffen K Rosahl; Vera van Velthoven; Ansgar Berlis; Carsten Christof Boedeker; Roland Laszig; Christian Barna Teszler; Gerd Jürgen Ridder
Journal:  J Otolaryngol       Date:  2006-12

6.  Endolymphatic sac carcinoma of the right petrous bone in Von Hippel-Lindau disease.

Authors:  D P Muzumdar; A Goel; S Fattepurkar; N Goel
Journal:  J Clin Neurosci       Date:  2006-05       Impact factor: 1.961

7.  Differential grading of endolymphatic sac tumor extension by virtue of von Hippel-Lindau disease status.

Authors:  Nicholas C Bambakidis; Cliff A Megerian; Robert A Ratcheson
Journal:  Otol Neurotol       Date:  2004-09       Impact factor: 2.311

8.  The radiologic diagnosis of endolymphatic sac tumors.

Authors:  Nirmal P Patel; Richard H Wiggins; Clough Shelton
Journal:  Laryngoscope       Date:  2006-01       Impact factor: 3.325

Review 9.  Endolymphatic sac tumor (low-grade papillary adenocarcinoma) of the temporal bone.

Authors:  Kenneth O Devaney; Alfio Ferlito; Alessandra Rinaldo
Journal:  Acta Otolaryngol       Date:  2003-12       Impact factor: 1.494

10.  Mechanisms of morbid hearing loss associated with tumors of the endolymphatic sac in von Hippel-Lindau disease.

Authors:  John A Butman; H Jeffrey Kim; Martin Baggenstos; Joshua M Ammerman; James Dambrosia; Athos Patsalides; Nicholas J Patronas; Edward H Oldfield; Russell R Lonser
Journal:  JAMA       Date:  2007-07-04       Impact factor: 56.272

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  1 in total

1.  High-resolution MRI of the inner ear enables syndrome differentiation and specific treatment of cerebellar downbeat nystagmus and secondary endolymphatic hydrops in a postoperative ELST patient.

Authors:  V Kirsch; B Ertl-Wagner; A Berman; J Gerb; M Dieterich; S Becker-Bense
Journal:  J Neurol       Date:  2018-04-11       Impact factor: 4.849

  1 in total

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