Double aortic arch with ascending aortic aneurysm and aortic valve regurgitation.

Double aortic arch is a rare congenital great vessel anomaly. We report a 21-year-old man who was diagnosed with a double aortic arch combining with ascending aortic aneurysm and aortic valve regurgitation. Computerized tomographic angiography and echocardiogram confirmed the diagnosis before operation. The patient underwent aortic root replacement and artificial vessel construction. At 3 years' follow-up, the patient continues to have a good surgical recovery, although long-term results need observing. A review of the literature shows no double aortic arch combination with ascending aortic aneurysm and aortic regurgitation has been reported so far.