Literature DB >> 24387990

Mutations in PCYT1A, encoding a key regulator of phosphatidylcholine metabolism, cause spondylometaphyseal dysplasia with cone-rod dystrophy.

Julie Hoover-Fong1, Nara Sobreira2, Julie Jurgens3, Peggy Modaff4, Carrie Blout5, Ann Moser6, Ok-Hwa Kim7, Tae-Joon Cho8, Sung Yoon Cho9, Sang Jin Kim10, Dong-Kyu Jin11, Hiroshi Kitoh12, Woong-Yang Park13, Hua Ling14, Kurt N Hetrick14, Kimberly F Doheny14, David Valle15, Richard M Pauli4.   

Abstract

Entities:  

Mesh:

Substances:

Year:  2014        PMID: 24387990      PMCID: PMC3882727          DOI: 10.1016/j.ajhg.2013.11.018

Source DB:  PubMed          Journal:  Am J Hum Genet        ISSN: 0002-9297            Impact factor:   11.025


× No keyword cloud information.
  48 in total

1.  Predicting the effects of coding non-synonymous variants on protein function using the SIFT algorithm.

Authors:  Prateek Kumar; Steven Henikoff; Pauline C Ng
Journal:  Nat Protoc       Date:  2009-06-25       Impact factor: 13.491

2.  Titin mutations as the molecular basis for dilated cardiomyopathy.

Authors:  Manatsu Itoh-Satoh; Takeharu Hayashi; Hirofumi Nishi; Yoshinori Koga; Takuro Arimura; Takeshi Koyanagi; Megumi Takahashi; Shigeru Hohda; Kazuo Ueda; Tatsuhito Nouchi; Michiaki Hiroe; Fumiaki Marumo; Tsutomu Imaizumi; Michio Yasunami; Akinori Kimura
Journal:  Biochem Biophys Res Commun       Date:  2002-02-22       Impact factor: 3.575

3.  Early embryonic lethality in mice with targeted deletion of the CTP:phosphocholine cytidylyltransferase alpha gene (Pcyt1a).

Authors:  Limin Wang; Susan Magdaleno; Ira Tabas; Suzanne Jackowski
Journal:  Mol Cell Biol       Date:  2005-04       Impact factor: 4.272

4.  Structural analysis of the titin gene in hypertrophic cardiomyopathy: identification of a novel disease gene.

Authors:  M Satoh; M Takahashi; T Sakamoto; M Hiroe; F Marumo; A Kimura
Journal:  Biochem Biophys Res Commun       Date:  1999-08-27       Impact factor: 3.575

5.  The Sequence Alignment/Map format and SAMtools.

Authors:  Heng Li; Bob Handsaker; Alec Wysoker; Tim Fennell; Jue Ruan; Nils Homer; Gabor Marth; Goncalo Abecasis; Richard Durbin
Journal:  Bioinformatics       Date:  2009-06-08       Impact factor: 6.937

6.  Mutation analysis of PEX7 in 60 probands with rhizomelic chondrodysplasia punctata and functional correlations of genotype with phenotype.

Authors:  Nancy Braverman; Li Chen; Paul Lin; Cassandra Obie; Gary Steel; Pamela Douglas; Pranesh K Chakraborty; Joe T R Clarke; Avihu Boneh; Ann Moser; Hugo Moser; David Valle
Journal:  Hum Mutat       Date:  2002-10       Impact factor: 4.878

7.  The kinase domain of titin controls muscle gene expression and protein turnover.

Authors:  Stephan Lange; Fengqing Xiang; Andrey Yakovenko; Anna Vihola; Peter Hackman; Elena Rostkova; Jakob Kristensen; Birgit Brandmeier; Gereon Franzen; Birgitta Hedberg; Lars Gunnar Gunnarsson; Simon M Hughes; Sylvie Marchand; Thomas Sejersen; Isabelle Richard; Lars Edström; Elisabeth Ehler; Bjarne Udd; Mathias Gautel
Journal:  Science       Date:  2005-03-31       Impact factor: 47.728

8.  A framework for variation discovery and genotyping using next-generation DNA sequencing data.

Authors:  Mark A DePristo; Eric Banks; Ryan Poplin; Kiran V Garimella; Jared R Maguire; Christopher Hartl; Anthony A Philippakis; Guillermo del Angel; Manuel A Rivas; Matt Hanna; Aaron McKenna; Tim J Fennell; Andrew M Kernytsky; Andrey Y Sivachenko; Kristian Cibulskis; Stacey B Gabriel; David Altshuler; Mark J Daly
Journal:  Nat Genet       Date:  2011-04-10       Impact factor: 38.330

9.  Truncations of titin causing dilated cardiomyopathy.

Authors:  Daniel S Herman; Lien Lam; Matthew R G Taylor; Libin Wang; Polakit Teekakirikul; Danos Christodoulou; Lauren Conner; Steven R DePalma; Barbara McDonough; Elizabeth Sparks; Debbie Lin Teodorescu; Allison L Cirino; Nicholas R Banner; Dudley J Pennell; Sharon Graw; Marco Merlo; Andrea Di Lenarda; Gianfranco Sinagra; J Martijn Bos; Michael J Ackerman; Richard N Mitchell; Charles E Murry; Neal K Lakdawala; Carolyn Y Ho; Paul J R Barton; Stuart A Cook; Luisa Mestroni; J G Seidman; Christine E Seidman
Journal:  N Engl J Med       Date:  2012-02-16       Impact factor: 91.245

10.  Ensembl 2009.

Authors:  T J P Hubbard; B L Aken; S Ayling; B Ballester; K Beal; E Bragin; S Brent; Y Chen; P Clapham; L Clarke; G Coates; S Fairley; S Fitzgerald; J Fernandez-Banet; L Gordon; S Graf; S Haider; M Hammond; R Holland; K Howe; A Jenkinson; N Johnson; A Kahari; D Keefe; S Keenan; R Kinsella; F Kokocinski; E Kulesha; D Lawson; I Longden; K Megy; P Meidl; B Overduin; A Parker; B Pritchard; D Rios; M Schuster; G Slater; D Smedley; W Spooner; G Spudich; S Trevanion; A Vilella; J Vogel; S White; S Wilder; A Zadissa; E Birney; F Cunningham; V Curwen; R Durbin; X M Fernandez-Suarez; J Herrero; A Kasprzyk; G Proctor; J Smith; S Searle; P Flicek
Journal:  Nucleic Acids Res       Date:  2008-11-25       Impact factor: 16.971

View more
  27 in total

1.  Truncating mutations in the last exon of NOTCH3 cause lateral meningocele syndrome.

Authors:  Karen W Gripp; Katherine M Robbins; Nara L Sobreira; P Dane Witmer; Lynne M Bird; Kristiina Avela; Outi Makitie; Daniela Alves; Jacob S Hogue; Elaine H Zackai; Kimberly F Doheny; Deborah L Stabley; Katia Sol-Church
Journal:  Am J Med Genet A       Date:  2014-11-13       Impact factor: 2.802

Review 2.  Genetic diseases of the Kennedy pathways for membrane synthesis.

Authors:  Mahtab Tavasoli; Sarah Lahire; Taryn Reid; Maren Brodovsky; Christopher R McMaster
Journal:  J Biol Chem       Date:  2020-12-18       Impact factor: 5.157

Review 3.  Advances in Skeletal Dysplasia Genetics.

Authors:  Krista A Geister; Sally A Camper
Journal:  Annu Rev Genomics Hum Genet       Date:  2015-04-22       Impact factor: 8.929

4.  GeneMatcher aids in the identification of a new malformation syndrome with intellectual disability, unique facial dysmorphisms, and skeletal and connective tissue abnormalities caused by de novo variants in HNRNPK.

Authors:  P Y Billie Au; Jing You; A Micheil Innes; Antonie D Kline; Oana Caluseriu; Jeremy Schwartzentruber; Jacek Majewski; Francois P Bernier; Marcia Ferguson; David Valle; Jillian S Parboosingh; Nara Sobreira
Journal:  Hum Mutat       Date:  2015-08-06       Impact factor: 4.878

5.  Multiple sclerosis patient-derived CSF induces transcriptional changes in proliferating oligodendrocyte progenitors.

Authors:  Jeffery D Haines; Oscar G Vidaurre; Fan Zhang; Ángela L Riffo-Campos; Josefa Castillo; Bonaventura Casanova; Patrizia Casaccia; Gerardo Lopez-Rodas
Journal:  Mult Scler       Date:  2015-05-06       Impact factor: 6.312

Review 6.  Genetic Diseases of the Kennedy Pathway for Phospholipid Synthesis.

Authors:  Mahtab Tavasoli; Sarah Lahire; Taryn Reid; Maren Brodovsky; Christopher R McMaster
Journal:  J Biol Chem       Date:  2020-10-22       Impact factor: 5.157

7.  Interdomain communication in the phosphatidylcholine regulatory enzyme, CCTα, relies on a modular αE helix.

Authors:  Svetla G Taneva; Jaeyong Lee; Daniel G Knowles; Chanajai Tishyadhigama; Hongwen Chen; Rosemary B Cornell
Journal:  J Biol Chem       Date:  2019-09-04       Impact factor: 5.157

8.  Remodeling of the interdomain allosteric linker upon membrane binding of CCTα pulls its active site close to the membrane surface.

Authors:  Daniel G Knowles; Jaeyong Lee; Svetla G Taneva; Rosemary B Cornell
Journal:  J Biol Chem       Date:  2019-09-04       Impact factor: 5.157

9.  Defect in phosphoinositide signalling through a homozygous variant in PLCB3 causes a new form of spondylometaphyseal dysplasia with corneal dystrophy.

Authors:  Salma Ben-Salem; Sarah M Robbins; Nara Lm Sobreira; Angeline Lyon; Aisha M Al-Shamsi; Barira K Islam; Nadia A Akawi; Anne John; Pramathan Thachillath; Sania Al Hamed; David Valle; Bassam R Ali; Lihadh Al-Gazali
Journal:  J Med Genet       Date:  2017-11-09       Impact factor: 6.318

10.  New tools for Mendelian disease gene identification: PhenoDB variant analysis module; and GeneMatcher, a web-based tool for linking investigators with an interest in the same gene.

Authors:  Nara Sobreira; François Schiettecatte; Corinne Boehm; David Valle; Ada Hamosh
Journal:  Hum Mutat       Date:  2015-04       Impact factor: 4.878

View more

北京卡尤迪生物科技股份有限公司 © 2022-2023.