Literature DB >> 24384158

Oncologic outcome and urinary function after radical cystectomy for rhabdomyosarcoma in children: role of the orthotopic ileal neobladder based on 15-year experience at a single center.

Marco Castagnetti1, Lorenzo Angelini2, Rita Alaggio3, Giovanni Scarzello4, Gianni Bisogno5, Waifro Rigamonti2.   

Abstract

PURPOSE: We determined the oncologic and urological outcomes in patients with bladder/prostate rhabdomyosarcoma according to the type and timing of urinary tract surgery, with emphasis on the role of the Padua orthotopic ileal neobladder.
MATERIALS AND METHODS: We retrospectively analyzed oncologic and urological outcomes of 11 consecutive patients treated at our institution between 1998 and 2012.
RESULTS: Two patients underwent urethrectomy and placement of a heterotopic catheterizable ileal neobladder. The membranous urethra was preserved in 9 patients, 6 underwent primary Padua ileal neobladder at radical cystectomy, 2 underwent delayed Padua ileal neobladder and 1 underwent bilateral cutaneous ureterostomy. Four of these 9 patients experienced disease recurrence, including local recurrence in 2 despite negative intraoperative biopsies. Survivors undergoing heterotopic catheterizable ileal neobladder or primary Padua ileal neobladder learned to empty the bladder to completion without long-term upper tract deterioration. Both cases managed by delayed Padua ileal neobladder required clean intermittent catheterization eventually. Erections were reported in 5 of 6 surviving males.
CONCLUSIONS: The Padua ileal neobladder allowed preservation of volitional urethral voiding in all survivors in whom it was placed at radical cystectomy. Nevertheless, local recurrence was noted in 2 of the 9 cases where the membranous urethra was preserved. By comparison, patients undergoing delayed Padua ileal neobladder after attaining disease-free status never achieved voiding per urethra. Therefore, a heterotopic reservoir might be a more reliable choice under these circumstances. Erectile function is preserved in the majority of cases.
Copyright © 2014 American Urological Association Education and Research, Inc. Published by Elsevier Inc. All rights reserved.

Entities:  

Keywords:  cystectomy; prostate; rhabdomyosarcoma; urinary bladder; urinary diversion

Mesh:

Year:  2013        PMID: 24384158     DOI: 10.1016/j.juro.2013.12.040

Source DB:  PubMed          Journal:  J Urol        ISSN: 0022-5347            Impact factor:   7.450


  4 in total

Review 1.  Current Treatment of Pediatric Bladder and Prostate Rhabdomyosarcoma.

Authors:  Amanda F Saltzman; Nicholas G Cost
Journal:  Curr Urol Rep       Date:  2018-02-22       Impact factor: 3.092

2.  Determinants of Survival for Adolescents and Young Adults with Urothelial Bladder Cancer: Results from the California Cancer Registry.

Authors:  Joshua Lara; Ann Brunson; Theresa H M Keegan; Marcio Malogolowkin; Chong-Xian Pan; Stanley Yap; Ralph deVere White
Journal:  J Urol       Date:  2016-05-18       Impact factor: 7.450

3.  Appraisal of the role of radical prostatectomy for rhabdomyosarcoma in children: oncological and urological outcome.

Authors:  Lorenzo Angelini; Gianni Bisogno; Ciro Esposito; Marco Castagnetti
Journal:  Ther Adv Urol       Date:  2018-03-07

4.  Benefit of delayed primary excision in rhabdomyosarcoma: A report from the Children's Oncology Group.

Authors:  Timothy B Lautz; Yueh-Yun Chi; Minjie Li; Suzanne L Wolden; Dana L Casey; Jonathan C Routh; Candace F Granberg; Odion Binite; Erin R Rudzinski; Douglas S Hawkins; Rajkumar Venkatramani; David A Rodeberg
Journal:  Cancer       Date:  2020-10-20       Impact factor: 6.921

  4 in total

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