Literature DB >> 24378278

Portal hypertension and acute liver failure as uncommon manifestations of primary amyloidosis.

Blanca Norero1, Rosa María Pérez-Ayuso1, Ignacio Duarte2, Pablo Ramirez3, Alejandro Soza1, Marco Arrese1, Carlos Benítez1.   

Abstract

Hepatic involvement in primary amyloidosis is an infrequent challenge to the hepatologist. Although usually asymptomatic, amyloidosis may have unusual manifestations. Liver biopsy is an important diagnostic tool for this condition. Herein, we report three cases of portal hypertension related to primary hepatic amyloidosis, one of them in the form of acute liver failure.

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Year:  2013        PMID: 24378278

Source DB:  PubMed          Journal:  Ann Hepatol        ISSN: 1665-2681            Impact factor:   2.400


  5 in total

1.  Multiple myeloma with hepatic amyloid light-chain amyloidosis manifesting as progressive liver failure.

Authors:  Monique Oye; Kimberly Sanders; Maged Ghali; Ahmad Alkhasawneh
Journal:  BMJ Case Rep       Date:  2020-06-29

2.  Primary Hepatic Amyloidosis Presenting as Acute-on-Chronic Liver Failure.

Authors:  Madhumita Premkumar; Devaraja Rangegowda; Tanmay Vyas; Anand Kulkarni; Shrruti Grover; Rakhi Mahiwall; Shiv Kumar Sarin
Journal:  ACG Case Rep J       Date:  2017-02-15

3.  The clinical features and outcomes of systemic light chain amyloidosis with hepatic involvement.

Authors:  Liang Zhao; Guisheng Ren; Jinzhou Guo; Wencui Chen; Weiwei Xu; Xianghua Huang
Journal:  Ann Med       Date:  2022-12       Impact factor: 4.709

4.  Amyloidosis: an unusual cause of portal hypertension.

Authors:  Vilma Takayasu; Lorena Silva Laborda; Raquel Bernardelli; Henrique Trombini Pinesi; Marilia Polo Minguete E Silva; Viviane Chiavelli; Angélica Braz Simões; Aloisio Felipe-Silva
Journal:  Autops Case Rep       Date:  2016-06-30

5.  Portal Hypertension and a Stiff Liver.

Authors:  Felicia D'Alitto; Amina Scherz; Cristina Margini; Hendrik Von Tengg-Kobligk; Matteo Montani; Thomas Pabst; Annalisa Berzigotti
Journal:  Cureus       Date:  2018-06-08
  5 in total

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