Literature DB >> 24333062

Erythrocytapheresis compared with whole blood phlebotomy for the treatment of hereditary haemochromatosis.

Tatjana Sundic1, Tor Hervig2, Signe Hannisdal3, Jörg Assmus4, Rune J Ulvik5, Richard W Olaussen6, Sigbjørn Berentsen7.   

Abstract

BACKGROUND: Hereditary haemochromatosis may result in severe organ damage which can be prevented by therapy. We studied the possible advantages and disadvantages of erythrocytapheresis as compared with phlebotomy in patients with hereditary haemochromatosis.
MATERIALS AND METHODS: In a prospective, randomised, open-label study, patients with hereditary haemochromatosis were randomised to bi-weekly apheresis or weekly whole blood phlebotomy. Primary end-points were decrease in ferritin levels and transferrin saturation. Secondary endpoints were decrease in haemoglobin levels, discomfort during the therapeutic procedure, costs and technicians' working time.
RESULTS: Sixty-two patients were included. Thirty patients were randomised to apheresis and 32 to whole blood phlebotomy. Initially, ferritin levels declined more rapidly in the apheresis group, and the difference became statistically highly significant at 11 weeks; however, time to normalisation of ferritin level was equal in the two groups. We observed no significant differences in decline of transferrin saturation, haemoglobin levels or discomfort. The mean cumulative technician time consumption until the ferritin level reached 50 μg/L was longer in the apheresis group, but the difference was not statistically significant. The cumulative costs for materials until achievement of the desired ferritin levels were three-fold higher in the apheresis group.
CONCLUSION: Treatment of hereditary haemochromatosis with erythrocytapheresis instead of whole blood phlebotomy results in a more rapid initial decline in ferritin levels and a reduced number of procedures per patient, but not in earlier achievement of target ferritin level. The frequency of discomfort was equally low with the two methods. The costs and, probably, technician time consumption were higher in the apheresis group.

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Year:  2013        PMID: 24333062      PMCID: PMC3934269          DOI: 10.2450/2013.0128-13

Source DB:  PubMed          Journal:  Blood Transfus        ISSN: 1723-2007            Impact factor:   3.443


  20 in total

1.  Repeated isovolemic large-volume erythrocytapheresis in the treatment of idiopathic hemochromatosis.

Authors:  H Kellner; W G Zoller
Journal:  Z Gastroenterol       Date:  1992-11       Impact factor: 2.000

Review 2.  Screening for haemochromatosis.

Authors:  R J Ulvik
Journal:  Scand J Clin Lab Invest Suppl       Date:  1990

3.  Erythrocytapheresis versus phlebotomy in the initial treatment of HFE hemochromatosis patients: results from a randomized trial.

Authors:  Eva Rombout-Sestrienkova; Fred H M Nieman; Brigitte A B Essers; Paulus A H van Noord; Mirian C H Janssen; Cees Th B M van Deursen; Laurens P Bos; Ferdinand Rombout; Rogier van den Braak; Peter W de Leeuw; Ger H Koek
Journal:  Transfusion       Date:  2011-08-16       Impact factor: 3.157

4.  Erythrocytapheresis. A method for rapid extracorporeal elimination of erythrocytes. Results in 65 patients.

Authors:  W G Zoller; H Kellner; F A Spengel
Journal:  Klin Wochenschr       Date:  1988-05-02

5.  Erythrocytapheresis with recombinant human erythropoietin in hereditary hemochromatosis therapy: a new alternative.

Authors:  A Kohan; R Niborski; J Daruich; J Rey; F Bastos; G Amerise; R Herrera; M García; W Olivera; M T Santarelli; J S Avalos; J Findor
Journal:  Vox Sang       Date:  2000       Impact factor: 2.144

6.  Patient compliance with phlebotomy therapy for iron overload associated with hemochromatosis.

Authors:  Bret L Hicken; Diane C Tucker; James C Barton
Journal:  Am J Gastroenterol       Date:  2003-09       Impact factor: 10.864

7.  Persons with screening-detected haemochromatosis: as healthy as the general population?

Authors:  A Asberg; K Hveem; O Krüger; K S Bjerve
Journal:  Scand J Gastroenterol       Date:  2002-06       Impact factor: 2.423

Review 8.  Haemochromatosis: find them or forget about them?

Authors:  Paul C Adams
Journal:  Eur J Gastroenterol Hepatol       Date:  2004-09       Impact factor: 2.566

9.  Effectiveness of erythrocytapheresis in idiopathic hemochromatosis. Report of 14 cases.

Authors:  D Conte; C Mandelli; M Cesana; R Ferrini; M Marconi; A Bianchi
Journal:  Int J Artif Organs       Date:  1989-01       Impact factor: 1.595

10.  In hereditary hemochromatosis, red cell apheresis removes excess iron twice as fast as manual whole blood phlebotomy.

Authors:  J Muncunill; P Vaquer; A Galmés; A Obrador; M Parera; J Bargay; J Besalduch
Journal:  J Clin Apher       Date:  2002       Impact factor: 2.821

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  5 in total

Review 1.  Interventions for hereditary haemochromatosis: an attempted network meta-analysis.

Authors:  Elena Buzzetti; Maria Kalafateli; Douglas Thorburn; Brian R Davidson; Emmanuel Tsochatzis; Kurinchi Selvan Gurusamy
Journal:  Cochrane Database Syst Rev       Date:  2017-03-08

2.  Patients with hereditary hemochromatosis reach safe range of transferrin saturation sooner with erythrocytaphereses than with phlebotomies.

Authors:  Eva Rombout-Sestrienkova; Lloyd Brandts; Ger H Koek; Cees Th B M van Deursen
Journal:  J Clin Apher       Date:  2021-12-13       Impact factor: 2.605

3.  Safety and Efficacy of Therapeutic Erythrocytapheresis Treatment in Chronic Mountain Sickness Patients in Shigatse, Tibet, China.

Authors:  Mingyuan Niu; Shekhar Singh; Ma Mi; Pian Bian; Zhuoga Deji; Duoji Mima; Xiankai Li
Journal:  Med Sci Monit       Date:  2020-12-23

4.  Higher age at diagnosis of hemochromatosis is the strongest predictor of the occurrence of hepatocellular carcinoma in the Swiss hemochromatosis cohort: A prospective longitudinal observational study.

Authors:  Albina Nowak; Rebekka S Giger; Pierre-Alexandre Krayenbuehl
Journal:  Medicine (Baltimore)       Date:  2018-10       Impact factor: 1.817

5.  A predictive model for estimating the number of erythrocytapheresis or phlebotomy treatments for patients with naïve hereditary hemochromatosis.

Authors:  Eva Rombout-Sestrienkova; Bjorn Winkens; Marian van Kraaij; Cees Th B M van Deursen; Mirian C H Janssen; Alexander M J Rennings; Dorothea Evers; Jean-Louis Kerkhoffs; Ad Masclee; Ger H Koek
Journal:  J Clin Apher       Date:  2020-12-24       Impact factor: 2.821

  5 in total

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