| Literature DB >> 24298508 |
Ashish Shrivastava1, Akshara Gupta, Achal Gupta, Jyoti Shrivastava.
Abstract
The Peutz Jeghers syndrome (PJS) is an autosomal dominant disorder which is characterised by hamartomatous polyposes of the gastrointestinal tract, melanin pigmentation of the skin and mucous membranes, and an increased risk for cancer. We are reporting a case of a 15-year-old male with Peutz Jeghers syndrome, who presented to us with features of chronic intestinal obstruction and anaemia. Initially, patient was managed conservatively, but later on, an elective exploratory laparotomy was done for definitive management of intussusception. Laparotomy revealed a jejuno-jejunal intussusception with spontaneous recanalisation of gut which contained a long segment of gangrenous small bowel in the lumen. Resection and anastomosis of the jejunal segment was done. To the best of our knowledge, this might be the first case report on spontaneous recanalisation of small intestine.Entities:
Keywords: Peutz Jeghers syndrome; acute abdomen; hamartomatous polyp; intussusception; spontaneous recanalisation
Year: 2013 PMID: 24298508 PMCID: PMC3843420 DOI: 10.7860/JCDR/2013/5741.3503
Source DB: PubMed Journal: J Clin Diagn Res ISSN: 0973-709X