Literature DB >> 24296881

Immunopathological significance of ovarian teratoma in patients with anti-N-methyl-d-aspartate receptor encephalitis.

Emi Tabata1, Masanori Masuda, Makoto Eriguchi, Masatoshi Yokoyama, Yoshiyuki Takahashi, Keiko Tanaka, Motohiro Yukitake, Etsuo Horikawa, Hideo Hara.   

Abstract

BACKGROUND: The clinical importance of ovarian teratoma in anti-N-methyl-D-aspartate receptor (NMDAR) encephalitis has been established, however investigations of ovarian teratoma in patients with anti-NMDAR encephalitis remain limited.
OBJECTIVE: To clarify differences in NMDAR distribution and lymphocyte infiltration in ovarian teratoma between patients with and without anti-NMDAR encephalitis.
METHODS: Participants initially comprised 26 patients with ovarian teratomas. NMDAR distribution and lymphocyte infiltration in ovarian teratomas were examined using immunopathological techniques. Clinical, laboratory, and radiological data were compared between patients showing the features of encephalitis. Anti-NMDAR antibodies in the serum and cerebrospinal fluid were also measured in encephalitis patients.
RESULTS: Neuronal tissues were obtained from ovarian teratomas in 22 patients (after excluding 4 patients who did not satisfy the inclusion criteria), and the presence of NMDA receptor subunits was revealed in all patients. Lymphocyte infiltration was more frequent in the encephalitis group (n = 3) than in the non-encephalitis group. In particular, dense B-lymphocyte infiltration near neural tissues was observed in the encephalitis group.
CONCLUSIONS: Differences in lymphocyte infiltration in ovarian teratomas between anti-NMDAR encephalitis and non-encephalitis patients suggest the immunological importance of the ovarian teratoma as the site of antigen presentation in anti-NMDAR encephalitis.

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Year:  2013        PMID: 24296881     DOI: 10.1159/000353982

Source DB:  PubMed          Journal:  Eur Neurol        ISSN: 0014-3022            Impact factor:   1.710


  11 in total

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6.  Immunopathological characterization of ovarian teratomas associated with anti-N-methyl-D-aspartate receptor encephalitis.

Authors:  Aude Chefdeville; Isabelle Treilleux; Marie-Eve Mayeur; Coline Couillault; Géraldine Picard; Chloé Bost; Karima Mokhtari; Alexandre Vasiljevic; David Meyronet; Véronique Rogemond; Dimitri Psimaras; Bertrand Dubois; Jérôme Honnorat; Virginie Desestret
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9.  Co-expression of NMDA-receptor subunits NR1, NR2A, and NR2B in dysplastic neurons of teratomas in patients with paraneoplastic NMDA-receptor-encephalitis: a retrospective clinico-pathology study of 159 patients.

Authors:  Xin-Yue Jiang; Song Lei; Le Zhang; Xu Liu; Min-Tao Lin; Ingmar Blumcke; Yue-Shan Piao; Dong Zhou; Jin-Mei Li
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10.  Differential expression of antibodies to NMDA receptor in anti-NMDA receptor encephalitis and in neuropsychiatric systemic lupus erythematosus.

Authors:  Shunsei Hirohata; Keiko Tanaka
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