Literature DB >> 24292756

Anaplastic large cell lymphoma mimicking fibrosing mediastinitis.

Masato Taki1, Shinya Inada, Ryo Ariyasu, Yoshinobu Konishi, Natsumi Okamoto, Masanori Yoshida, Hiroaki Nagano, Kenji Hanaoka, Kazuhiko Nakagawa, Yasukiyo Nakamura, Chie Yoshimura, Toshiaki Wakayama, Yasuo Nishizaka, Tomoko Wakasa, Mitsuru Tsudo, Ryoichi Amitani.   

Abstract

Fibrosing mediastinitis is rare. One type of this disease is idiopathic fibrosing mediastinitis. It is necessary to rule out malignancy in order to accurately diagnose fibrosing mediastinitis. We herein report a case of anaplastic large cell lymphoma diagnosed three months after a preliminary diagnosis of fibrosing mediastinitis. Glucocorticoid therapy was not successful in controlling disease progression. Immediately after initiating chemotherapy for lymphoma, the patient's symptoms improved dramatically and the mediastinal lesion decreased in size. Although few similar cases have been reported, hidden malignancy may present as fibrosing mediastinitis. Therefore, physicians should consider the probability of malignancy in patients with fibrosing mediastinitis because treatments may vary accordingly.

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Year:  2013        PMID: 24292756     DOI: 10.2169/internalmedicine.52.1016

Source DB:  PubMed          Journal:  Intern Med        ISSN: 0918-2918            Impact factor:   1.271


  2 in total

1.  Mediastinal peripheral T-cell lymphoma diagnosed by repeated biopsies after an initial diagnosis of fibrosing mediastinitis.

Authors:  Naoko Kakuta; Mitsuhiro Sumitani; Arata Sugitani; Kenji Nakahama; Yuzo Miki; Seichi Syoji
Journal:  Respirol Case Rep       Date:  2017-09-18

Review 2.  An overview on the differential diagnostics of tumors of the anterior-superior mediastinum: the pathologist's perspective.

Authors:  Mirella Marino; Stefano Ascani
Journal:  Mediastinum       Date:  2019-02-22
  2 in total

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