| Literature DB >> 24292756 |
Masato Taki1, Shinya Inada, Ryo Ariyasu, Yoshinobu Konishi, Natsumi Okamoto, Masanori Yoshida, Hiroaki Nagano, Kenji Hanaoka, Kazuhiko Nakagawa, Yasukiyo Nakamura, Chie Yoshimura, Toshiaki Wakayama, Yasuo Nishizaka, Tomoko Wakasa, Mitsuru Tsudo, Ryoichi Amitani.
Abstract
Fibrosing mediastinitis is rare. One type of this disease is idiopathic fibrosing mediastinitis. It is necessary to rule out malignancy in order to accurately diagnose fibrosing mediastinitis. We herein report a case of anaplastic large cell lymphoma diagnosed three months after a preliminary diagnosis of fibrosing mediastinitis. Glucocorticoid therapy was not successful in controlling disease progression. Immediately after initiating chemotherapy for lymphoma, the patient's symptoms improved dramatically and the mediastinal lesion decreased in size. Although few similar cases have been reported, hidden malignancy may present as fibrosing mediastinitis. Therefore, physicians should consider the probability of malignancy in patients with fibrosing mediastinitis because treatments may vary accordingly.Entities:
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Year: 2013 PMID: 24292756 DOI: 10.2169/internalmedicine.52.1016
Source DB: PubMed Journal: Intern Med ISSN: 0918-2918 Impact factor: 1.271