Literature DB >> 24247759

Symptom burden in persons with myotonic and facioscapulohumeral muscular dystrophy.

Amanda E Smith1, Kara McMullen, Mark P Jensen, Gregory T Carter, Ivan R Molton.   

Abstract

OBJECTIVE: This study examines the prevalence of pain, fatigue, imbalance, memory impairment, and vision loss in persons with myotonic and facioscapulohumeral dystrophy and their association with functioning.
DESIGN: A survey (N = 170) included measures of severity (0-10 scales) and course of these symptoms as well as measures of social integration, home competency, mental health, and productive activity. Descriptive and regression analyses examined the associations between symptoms and functioning.
RESULTS: Fatigue (91%), imbalance (82%), and pain (77%) were the most commonly reported. The most severe symptom was fatigue (mean ± SD severity, 5.14 ± 2.81), followed by imbalance (4.95 ± 3.25). Symptoms were most likely to stay the same or worsen since onset. Controlling for potential medical and demographic confounds, symptoms were associated with 17% of the mental health variance, 10% of home competency, 10% of social integration, 16% of productive activity for myotonic dystrophy type 1, and 12% of productive activity for facioscapulohumeral muscular dystrophy.
CONCLUSIONS: Pain, fatigue, and imbalance are common in persons with muscular dystrophy. Interventions may be useful to mitigate their impact on functioning. Further research should examine these relationships to guide clinical practices.

Entities:  

Mesh:

Year:  2014        PMID: 24247759      PMCID: PMC3991729          DOI: 10.1097/PHM.0000000000000032

Source DB:  PubMed          Journal:  Am J Phys Med Rehabil        ISSN: 0894-9115            Impact factor:   2.159


  19 in total

1.  Role of disease severity, illness perceptions, and mood on quality of life in muscle disease.

Authors:  Michael R Rose; Reza Sadjadi; John Weinman; Tayyaba Akhtar; Shree Pandya; John T Kissel; Carlayne E Jackson
Journal:  Muscle Nerve       Date:  2012-09       Impact factor: 3.217

2.  Six patient-reported outcome measurement information system short form measures have negligible age- or diagnosis-related differential item functioning in individuals with disabilities.

Authors:  Karon F Cook; Alyssa M Bamer; Dagmar Amtmann; Ivan R Molton; Mark P Jensen
Journal:  Arch Phys Med Rehabil       Date:  2012-03-02       Impact factor: 3.966

3.  Effects of pain and fatigue on physical functioning and depression in persons with muscular dystrophy.

Authors:  Kevin N Alschuler; Mark P Jensen; Mark C Goetz; Amanda E Smith; Aimee M Verrall; Ivan R Molton
Journal:  Disabil Health J       Date:  2012-08-04       Impact factor: 2.554

4.  Muscle pain as a prominent feature of facioscapulohumeral muscular dystrophy (FSHD): four illustrative case reports.

Authors:  K M Bushby; C Pollitt; M A Johnson; M T Rogers; P F Chinnery
Journal:  Neuromuscul Disord       Date:  1998-12       Impact factor: 4.296

5.  Chronic pain in persons with neuromuscular disease.

Authors:  Mark P Jensen; Richard T Abresch; Gregory T Carter; Craig M McDonald
Journal:  Arch Phys Med Rehabil       Date:  2005-06       Impact factor: 3.966

6.  The Community Integration Questionnaire revisited: an assessment of factor structure and validity.

Authors:  A M Sander; K L Fuchs; W M High; K M Hall; J S Kreutzer; M Rosenthal
Journal:  Arch Phys Med Rehabil       Date:  1999-10       Impact factor: 3.966

7.  Assessment of pain and health-related quality of life in slowly progressive neuromuscular disease.

Authors:  Richard T Abresch; Gregory T Carter; Mark P Jensen; David D Kilmer
Journal:  Am J Hosp Palliat Care       Date:  2002 Jan-Feb       Impact factor: 2.500

8.  Pain in youths with neuromuscular disease.

Authors:  Joyce M Engel; Deborah Kartin; Gregory T Carter; Mark P Jensen; Kenneth M Jaffe
Journal:  Am J Hosp Palliat Care       Date:  2009 Oct-Nov       Impact factor: 2.500

9.  Epidemiology and pathophysiology of falls in facioscapulohumeral disease.

Authors:  C G C Horlings; M Munneke; A Bickerstaffe; L Laverman; J H J Allum; G W A M Padberg; B R Bloem; B G M van Engelen
Journal:  J Neurol Neurosurg Psychiatry       Date:  2009-06-21       Impact factor: 10.154

Review 10.  Fatigue in neurological disorders.

Authors:  Abhijit Chaudhuri; Peter O Behan
Journal:  Lancet       Date:  2004-03-20       Impact factor: 79.321

View more
  6 in total

1.  Medication adherence in patients with myotonic dystrophy and facioscapulohumeral muscular dystrophy.

Authors:  Bryan P Fitzgerald; Kelly M Conn; Joanne Smith; Andrew Walker; Amy L Parkhill; James E Hilbert; Elizabeth A Luebbe; Richard T Moxley
Journal:  J Neurol       Date:  2016-10-12       Impact factor: 4.849

2.  What Determines Whether a Pain is Rated as Mild, Moderate, or Severe? The Importance of Pain Beliefs and Pain Interference.

Authors:  Mark P Jensen; Catarina Tomé-Pires; Rocío de la Vega; Santiago Galán; Ester Solé; Jordi Miró
Journal:  Clin J Pain       Date:  2017-05       Impact factor: 3.442

Review 3.  Pharmacological treatment of chronic non-cancer pain in pediatric patients.

Authors:  Eapen Mathew; Eugene Kim; Kenneth R Goldschneider
Journal:  Paediatr Drugs       Date:  2014-12       Impact factor: 3.022

4.  Noninvasive assessment of respiratory muscle strength and activity in Myotonic dystrophy.

Authors:  Morgana de Araújo Evangelista; Fernando Augusto Lavezzo Dias; Mário Emílio Teixeira Dourado Júnior; George Carlos do Nascimento; Antonio Sarmento; Lucien Peroni Gualdi; Andrea Aliverti; Vanessa Resqueti; Guilherme Augusto de Freitas Fregonezi
Journal:  PLoS One       Date:  2017-06-08       Impact factor: 3.240

5.  Pain in adult myotonic dystrophy type 1: relation to function and gender.

Authors:  Gro Solbakken; Sissel Løseth; Anne Froholdt; Torunn D Eikeland; Terje Nærland; Jan C Frich; Espen Dietrichs; Kristin Ørstavik
Journal:  BMC Neurol       Date:  2021-03-04       Impact factor: 2.474

6.  Multidimensional aspects of pain in myotonic dystrophies.

Authors:  Marina Peric; Stojan Peric; Nada Rapajic; Valerija Dobricic; Dusanka Savic-Pavicevic; Ivana Nesic; Svetlana Radojicic; Ivana Novakovic; Dragana Lavrnic; Vidosava Rakocevic-Stojanovic
Journal:  Acta Myol       Date:  2015-12
  6 in total

北京卡尤迪生物科技股份有限公司 © 2022-2023.