Literature DB >> 24027376

Biventricular noncompaction presented with symptomatic complete heart block - Report of a case and review of literature.

Soumya Patra1, Basant Kumar, Kanchanahalli Siddegowda Sadananda, Harsha Basappa, Manjunath Cholenahally Nanjappa.   

Abstract

Ventricular noncompaction has been recognized as a distinct form of rare cardiomyopathy characterized by numerous, prominent ventricular trabeculations and deep intertrabecular recesses and is caused by a disorder of endomyocardial morphogenesis. Concomitance of either valvular pathologies or complete atrioventricular block with biventricular noncompaction has rarely been reported. Herein, we present a case of 67 years old male presented with syncopal attack and congestive heart failure due to biventricular noncompaction with significant left ventricular dysfunction associated with complete atrioventricular block. He was formerly diagnosed as dilated cardiomyopathy for last 2 years. Review of literatures of all reported cases has been discussed.

Entities:  

Keywords:  Atrioventricular block; Noncompaction; Ventricle

Year:  2013        PMID: 24027376      PMCID: PMC3770114          DOI: 10.1016/j.jcdr.2013.03.003

Source DB:  PubMed          Journal:  J Cardiovasc Dis Res        ISSN: 0975-3583


  10 in total

1.  An adult patient with isolated left ventricular noncompaction presented with atrial fibrillation and complete atrioventricular block.

Authors:  Zhi-Qiang Ying; Geng Xu
Journal:  Intern Med       Date:  2011-11-01       Impact factor: 1.271

2.  Young male with isolated noncompaction of the ventricular myocardium presenting with atrial fibrillation and complete heart block.

Authors:  C G Sajeev; Johnson Francis; Vikram Shanker; Babu Vasudev; S Abdul Khader; K Venugopal
Journal:  Int J Cardiol       Date:  2006-02-08       Impact factor: 4.164

Review 3.  Left ventricular non-compaction revisited: a distinct phenotype with genetic heterogeneity?

Authors:  Erwin Oechslin; Rolf Jenni
Journal:  Eur Heart J       Date:  2011-01-31       Impact factor: 29.983

4.  Electrocardiographic findings at initial diagnosis in children with isolated left ventricular noncompaction.

Authors:  Yakup Ergul; Kemal Nisli; Muhammet Ali Varkal; Naci Oner; Memduh Dursun; Aygun Dindar; Umrah Aydogan; Rukiye Eker Omeroglu
Journal:  Ann Noninvasive Electrocardiol       Date:  2011-04       Impact factor: 1.468

5.  Biventricular myocardial noncompaction presenting with complete atrioventricular block.

Authors:  Ali Yildiz; Ozcan Ozeke; Selahattin Akyol; Recep Demirbag; Remzi Yilmaz; Mustafa Gur
Journal:  Int J Cardiol       Date:  2007-11-19       Impact factor: 4.164

6.  Complete atrioventricular block as the first manifestation of noncompaction of the ventricular myocardium.

Authors:  Bruno Ramos Nascimento; Daniel Furtado Vidigal; Renata De Carvalho Bicalho Carneiro; Warley Cristiano De Souza; Walkiria Monteiro Lopes; Antonio Luiz Pinho Ribeiro; E Maria Do Carmo Pereira Nunes
Journal:  Pacing Clin Electrophysiol       Date:  2011-03-16       Impact factor: 1.976

7.  Loss of function of hNav1.5 by a ZASP1 mutation associated with intraventricular conduction disturbances in left ventricular noncompaction.

Authors:  Yutao Xi; Tomohiko Ai; Enno De Lange; Zhaohui Li; Geru Wu; Luca Brunelli; W Buck Kyle; Isik Turker; Jie Cheng; Michael J Ackerman; Akinori Kimura; James N Weiss; Zhilin Qu; Jeffrey J Kim; Georgine Faulkner; Matteo Vatta
Journal:  Circ Arrhythm Electrophysiol       Date:  2012-08-28

8.  Electrocardiographic characteristics at initial diagnosis in patients with isolated left ventricular noncompaction.

Authors:  Jan Steffel; Richard Kobza; Erwin Oechslin; Rolf Jenni; Firat Duru
Journal:  Am J Cardiol       Date:  2009-10-01       Impact factor: 2.778

9.  Noncompaction of ventricular myocardium, complete atrioventricular block and minor congenital heart abnormalities: case report of an unusual coexistence.

Authors:  Bahadir Dağdeviren; Mehmet Eren; Enis Oguz
Journal:  Acta Cardiol       Date:  2002-06       Impact factor: 1.718

10.  Disappearance of left ventricular hypertrabeculation/noncompaction after biventricular pacing in a patient with polyneuropathy.

Authors:  Claudia Stöllberger; Hans Keller; Josef Finsterer
Journal:  J Card Fail       Date:  2007-04       Impact factor: 5.712

  10 in total

北京卡尤迪生物科技股份有限公司 © 2022-2023.