Literature DB >> 24010117

A case of rapunzel syndrome.

Joon Sung Kim1, Chang Woo Nam.   

Abstract

Rapunzel syndrome refers to a very rare condition in which swallowed hair forms a gastric trichobezoar that has a long tail extending into the small bowel. We describe a case of Rapunzel syndrome in an 8-year-old girl who presented with abdominal mass, epigastric pain and vomiting. Abdominal computed tomography scan showed a markedly dilated stomach filled with coarse heterogeneous materials. Upper gastrointestinal endoscopy revealed a huge hairy ball with a tail extending through the pylorus. We performed a surgical laparotomy and successfully removed a huge trichobezoar with a long tail extending into the middle portion of jejunum. Psychiatric consultation with review showed her past history of trichotillomania and trichophagia 4 years ago. But her parents denied further psychiatric therapy and she was lost to the follow-up. Rapunzel syndrome should be included in the differential diagnosis in children with chronic abdominal pain and trichophagia.

Entities:  

Keywords:  Abdominal pain; Bezoars; Rapunzel syndrome; Trichophagia; Trichotillomania

Year:  2013        PMID: 24010117      PMCID: PMC3760701          DOI: 10.5223/pghn.2013.16.2.127

Source DB:  PubMed          Journal:  Pediatr Gastroenterol Hepatol Nutr        ISSN: 2234-8840


  13 in total

1.  Gastric perforation secondary to recurrent trichobezoar.

Authors:  G Singh; S K Mitra
Journal:  Indian J Pediatr       Date:  1996 Sep-Oct       Impact factor: 1.967

2.  Huge gastric trichobezoar in a 10-year-old girl: case report with emphasis on endoscopy in diagnosis and therapy.

Authors:  A De Backer; V Van Nooten; Y Vandenplas
Journal:  J Pediatr Gastroenterol Nutr       Date:  1999-05       Impact factor: 2.839

3.  Gastric outlet obstruction secondary to a large trichobezoar.

Authors:  Aaron R Jensen; Christine T Trankiem; Steve Lebovitch; Harsh Grewal
Journal:  J Pediatr Surg       Date:  2005-08       Impact factor: 2.545

4.  Rapunzel syndrome: the unsuspected culprit.

Authors:  Mohammad Ezzedien Rabie; Abdul Rahman Arishi; Ashraf Khan; Hussein Ageely; Gaffar Abbas Seif El-Nasr; Mohammad Fagihi
Journal:  World J Gastroenterol       Date:  2008-02-21       Impact factor: 5.742

5.  CT appearances of the Rapunzel syndrome: an unusual form of bezoar and gastrointestinal obstruction.

Authors:  W M West; N D Duncan
Journal:  Pediatr Radiol       Date:  1998-05

6.  The Rapunzel syndrome. An unusual complication of intestinal bezoar.

Authors:  E D Vaughan; J L Sawyers; H W Scott
Journal:  Surgery       Date:  1968-02       Impact factor: 3.982

7.  Rapunzel syndrome with a fatal outcome in a neglected child.

Authors:  Denise Estefan Ventura; Fernando A Mardiros Herbella; Sergio T Schettini; Carlos Delmonte
Journal:  J Pediatr Surg       Date:  2005-10       Impact factor: 2.545

Review 8.  Rapunzel syndrome reviewed and redefined.

Authors:  Saleem Naik; Vivek Gupta; Swati Naik; Ashwin Rangole; Ashok K Chaudhary; Prashant Jain; Ashok K Sharma
Journal:  Dig Surg       Date:  2007-04-27       Impact factor: 2.588

Review 9.  Rapunzel syndrome: a comprehensive review of an unusual case of trichobezoar.

Authors:  Veena Gonuguntla; Divya-Devi Joshi
Journal:  Clin Med Res       Date:  2009-07-22

10.  Laparoscopic removal of a gastric trichobezoar in a pediatric patient.

Authors:  Jason D Fraser; Charles M Leys; Shawn D St Peter
Journal:  J Laparoendosc Adv Surg Tech A       Date:  2009-12       Impact factor: 1.878

View more
  4 in total

1.  Rapunzel syndrome: a rare cause of hypoproteinaemia and review of literature.

Authors:  Waqas Ullah; Kaiser Saleem; Ejaz Ahmad; Faiz Anwer
Journal:  BMJ Case Rep       Date:  2016-09-26

2.  Trichophagia along with trichobezoar in the absence of trichotillomania.

Authors:  Aseem Mehra; Ajit Avasthi; Vikas Gupta; Sandeep Grover
Journal:  J Neurosci Rural Pract       Date:  2014-11

3.  Gastrojejunal Enteral Tube Serving as a Small Bowel Bezoar Nidus.

Authors:  Derek G Armstrong; Isha Kaul; Jose A Hernandez; Bruno P Chumpitazi
Journal:  Cureus       Date:  2021-05-27

4.  Trichobezoar Causing Airway Compromise during Esophagogastroduodenoscopy.

Authors:  Erica Y Kao; Nicholas J Scalzitti; Gregory R Dion; Sarah N Bowe
Journal:  Case Rep Med       Date:  2015-09-17
  4 in total

北京卡尤迪生物科技股份有限公司 © 2022-2023.