| Literature DB >> 23901184 |
Ibrahim Aliyu1, Mohammad Aminu Mohammad.
Abstract
Pentalogy of Cantrell is a rare congenital malformation whose exact cause is not completely understood; it is characterized by defects in the anterior abdominal and thoracic walls consisting of omphalocoele, diaphragmatic defect, ectopia cordis, intracardiac defects and sternal clefts. The complex has variable clinical expression with complete and incomplete expressions reported. We, therefore, report a case of complete manifestation of the pentad in a 9-month-old boy.Entities:
Keywords: Cantrell; ectopia cordis; omphalocoele; pentalogy; sternal cleft
Year: 2013 PMID: 23901184 PMCID: PMC3719249 DOI: 10.4103/0300-1652.114576
Source DB: PubMed Journal: Niger Med J ISSN: 0300-1652