Literature DB >> 2388640

Paroxysmal kinesigenic dystonic choreoathetosis associated with a thalamic infarct.

A Camac1, P Greene, A Khandji.   

Abstract

We describe a patient with the development of paroxysmal kinesigenic dystonic choreoathetosis (PKDC) after a thalamic infarct. PKDC consists of brief episodes of dystonia or choreoathetosis triggered by movement. PKDC improves with anticonvulsants, and in some cases, with L-Dopa or anticholinergics. We review PKDC, and relate its salient features to idiopathic and secondary torsion dystonia. We postulate a similar underlying pathophysiology.

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Year:  1990        PMID: 2388640     DOI: 10.1002/mds.870050309

Source DB:  PubMed          Journal:  Mov Disord        ISSN: 0885-3185            Impact factor:   10.338


  6 in total

1.  Thalamic involvement in paroxysmal kinesigenic dyskinesia: a combined structural and diffusion tensor MRI analysis.

Authors:  Ji Hyun Kim; Dong-Wook Kim; Jung Bin Kim; Sang-Il Suh; Seong-Beom Koh
Journal:  Hum Brain Mapp       Date:  2014-12-11       Impact factor: 5.038

2.  Post-stroke movement disorders: report of 56 patients.

Authors:  F Alarcón; J C M Zijlmans; G Dueñas; N Cevallos
Journal:  J Neurol Neurosurg Psychiatry       Date:  2004-11       Impact factor: 10.154

3.  The thalamic ultrastructural abnormalities in paroxysmal kinesigenic choreoathetosis: a diffusion tensor imaging study.

Authors:  Bo Zhou; Qin Chen; Qiyong Gong; Hehan Tang; Dong Zhou
Journal:  J Neurol       Date:  2009-12-11       Impact factor: 4.849

4.  Arm Posturing in a Patient Following Stroke: Dystonia, Levitation, Synkinesis, or Spasticity?

Authors:  Krithi Irmady; Bahman Jabbari; Elan D Louis
Journal:  Tremor Other Hyperkinet Mov (N Y)       Date:  2015-12-11

5.  Mutations in the gene PRRT2 cause paroxysmal kinesigenic dyskinesia with infantile convulsions.

Authors:  Hsien-Yang Lee; Yong Huang; Nadine Bruneau; Patrice Roll; Elisha D O Roberson; Mark Hermann; Emily Quinn; James Maas; Robert Edwards; Tetsuo Ashizawa; Betul Baykan; Kailash Bhatia; Susan Bressman; Michiko K Bruno; Ewout R Brunt; Roberto Caraballo; Bernard Echenne; Natalio Fejerman; Steve Frucht; Christina A Gurnett; Edouard Hirsch; Henry Houlden; Joseph Jankovic; Wei-Ling Lee; David R Lynch; Shehla Mohammed; Ulrich Müller; Mark P Nespeca; David Renner; Jacques Rochette; Gabrielle Rudolf; Shinji Saiki; Bing-Wen Soong; Kathryn J Swoboda; Sam Tucker; Nicholas Wood; Michael Hanna; Anne M Bowcock; Pierre Szepetowski; Ying-Hui Fu; Louis J Ptáček
Journal:  Cell Rep       Date:  2011-12-15       Impact factor: 9.423

6.  Disruption of gray matter morphological networks in patients with paroxysmal kinesigenic dyskinesia.

Authors:  Xiuli Li; Du Lei; Running Niu; Lei Li; Xueling Suo; Wenbin Li; Chen Yang; Tianhua Yang; Jiechuan Ren; Walter H L Pinaya; Dong Zhou; Graham J Kemp; Qiyong Gong
Journal:  Hum Brain Mapp       Date:  2020-10-15       Impact factor: 5.399

  6 in total

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