Literature DB >> 23842565

Adrenoleukodystrophy and the mitochondrial connection: clues for supplementing Lorenzo's oil.

Carlos T Moraes1.   

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Year:  2013        PMID： 23842565      PMCID： PMC3722355          DOI： 10.1093/brain/awt189

Source DB:  PubMed          Journal:  Brain        ISSN： 0006-8950            Impact factor:   13.501


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  13 in total

Review 1.  The mitochondrial UPR - protecting organelle protein homeostasis.

Authors:  Cole M Haynes; David Ron
Journal:  J Cell Sci       Date:  2010-11-15       Impact factor: 5.285

Review 2.  X-linked adrenoleukodystrophy: clinical, biochemical and pathogenetic aspects.

Authors:  Johannes Berger; Jutta Gärtner
Journal:  Biochim Biophys Acta       Date:  2006-07-26

Review 3.  PGC-1α at the intersection of bioenergetics regulation and neuron function: from Huntington's disease to Parkinson's disease and beyond.

Authors:  Taiji Tsunemi; Albert R La Spada
Journal:  Prog Neurobiol       Date:  2011-11-09       Impact factor: 11.685

4.  Pioglitazone halts axonal degeneration in a mouse model of X-linked adrenoleukodystrophy.

Authors:  Laia Morató; Jorge Galino; Montserrat Ruiz; Noel Ylagan Calingasan; Anatoly A Starkov; Magali Dumont; Alba Naudí; Juan José Martínez; Patrick Aubourg; Manuel Portero-Otín; Reinald Pamplona; Elena Galea; M Flint Beal; Isidre Ferrer; Stéphane Fourcade; Aurora Pujol
Journal:  Brain       Date:  2013-06-22       Impact factor: 13.501

5.  Pharmacologic activation of mitochondrial biogenesis exerts widespread beneficial effects in a transgenic mouse model of Huntington's disease.

Authors:  Ashu Johri; Noel Y Calingasan; Thomas M Hennessey; Abhijeet Sharma; Lichuan Yang; Elizabeth Wille; Abhishek Chandra; M Flint Beal
Journal:  Hum Mol Genet       Date:  2011-11-17       Impact factor: 6.150

6.  MitoNEET is a uniquely folded 2Fe 2S outer mitochondrial membrane protein stabilized by pioglitazone.

Authors:  Mark L Paddock; Sandra E Wiley; Herbert L Axelrod; Aina E Cohen; Melinda Roy; Edward C Abresch; Dominique Capraro; Anne N Murphy; Rachel Nechushtai; Jack E Dixon; Patricia A Jennings
Journal:  Proc Natl Acad Sci U S A       Date:  2007-08-31       Impact factor: 11.205

Review 7.  Mitochondrial biogenesis and healthy aging.

Authors:  Guillermo López-Lluch; Pablo M Irusta; Placido Navas; Rafael de Cabo
Journal:  Exp Gerontol       Date:  2008-07-09       Impact factor: 4.032

8.  Toxic effects of X-linked adrenoleukodystrophy-associated, very long chain fatty acids on glial cells and neurons from rat hippocampus in culture.

Authors:  Sabine Hein; Peter Schönfeld; Stefan Kahlert; Georg Reiser
Journal:  Hum Mol Genet       Date:  2008-03-14       Impact factor: 6.150

9.  Activation of the PPAR/PGC-1alpha pathway prevents a bioenergetic deficit and effectively improves a mitochondrial myopathy phenotype.

Authors:  Tina Wenz; Francisca Diaz; Bruce M Spiegelman; Carlos T Moraes
Journal:  Cell Metab       Date:  2008-09       Impact factor: 27.287

10.  Putative X-linked adrenoleukodystrophy gene shares unexpected homology with ABC transporters.

Authors:  J Mosser; A M Douar; C O Sarde; P Kioschis; R Feil; H Moser; A M Poustka; J L Mandel; P Aubourg
Journal:  Nature       Date:  1993-02-25       Impact factor: 49.962
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  1 in total

1.  Spastic paraplegia as the predominant phenotype in a cohort of Chinese patients with adrenoleukodystrophy.

Authors:  Wen-Jiao Luo; Qiao Wei; Hai-Lin Dong; Yang-Tian Yan; Mei-Jiao Chen; Hong-Fu Li
Journal:  Mol Genet Genomic Med       Date:  2019-11-27       Impact factor: 2.183
  1 in total

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