Literature DB >> 23811305

Steroids in biliary atresia: single surgeon, single centre, prospective study.

Mark Davenport1, Chris Parsons, Sarah Tizzard, Nedim Hadzic.   

Abstract

BACKGROUND & AIMS: The effect of adjuvant steroids in infants with biliary atresia (BA) is not clear and evidence of benefit is lacking.
METHODS: During the period Jan. 2000-Dec. 2011, 153 infants with isolated (CMV IgM-ve) BA underwent Kasai portoenterostomy (KPE) at<70 days. They were divided into three groups: LOW-dose steroid (from a previous randomized trial; starting prednisolone 2mg/kg/day, n=18), HIGH-dose steroid (starting prednisolone 5mg/kg/day, n=44), and NO steroid [n=72+19 placebo (from randomized trial)=91]. Outcome was assessed by early liver biochemistry, clearance of jaundice (<20 μmol/L), and actuarial native liver survival. Data are quoted as median (IQ range) and compared with non-parametric ANOVA, Chi or Log-rank tests as appropriate. p ≤ 0.05 was regarded as significant.
RESULTS: All three groups were comparable for age (ANOVA, p=0.31) and a surrogate marker of liver fibrosis [aspartate-aminotransferase index (APRi), ANOVA, p=0.67]. At 1 month post KPE, there was a significant reduction in bilirubin [58 (25-91) vs. 91 (52-145)μmol/L, p=0.0015], AST [118 (91-159) vs. 155 (108-193)IU/L, p=0.0015], and APRi [0.49 (0.28-0.89) vs. 0.82 (0.45-1.2), p=0.005] for HIGH vs. NO steroid. There was a significant increase in % clearance of jaundice with the use of steroids [47/91 (52%) vs. 12/18 (67%) vs. 29/44 (66%); steroids vs. no steroids, p=0.037]. There was no statistical difference in 4-year patient survival (96% vs. 94% vs. 95%) or native liver survival (4 year=46% vs. 50 vs. 57%).
CONCLUSIONS: The adjuvant use of prednisolone significantly improved early post-operative liver biochemistry (especially at the higher dose), and increased the proportion of infants who cleared their jaundice at 6 months post-KPE. Crown
Copyright © 2013. Published by Elsevier B.V. All rights reserved.

Entities:  

Keywords:  APRi; AST; BA; BASM; Biliary Atresia Splenic Malformation; Biliary atresia; CMV; HLA; IBA; KPE; Kasai portoenterostomy; LT; NLS; Prognosis; Steroids; aspartate aminotransferase; aspartate aminotransferase-to-platelet ratio index; biliary atresia; cytomegalovirus; human leucocyte antigen; isolated biliary atresia; liver transplantation; native liver survival; γ-glutamyl transpeptidase; γGT

Mesh:

Substances:

Year:  2013        PMID: 23811305     DOI: 10.1016/j.jhep.2013.06.012

Source DB:  PubMed          Journal:  J Hepatol        ISSN: 0168-8278            Impact factor:   25.083


  19 in total

Review 1.  Pathogenesis of biliary atresia: defining biology to understand clinical phenotypes.

Authors:  Akihiro Asai; Alexander Miethke; Jorge A Bezerra
Journal:  Nat Rev Gastroenterol Hepatol       Date:  2015-05-26       Impact factor: 46.802

2.  Developmental histology of the portal plate in biliary atresia: observations and implications.

Authors:  Enrico La Pergola; Yoh Zen; Mark Davenport
Journal:  Pediatr Surg Int       Date:  2021-03-01       Impact factor: 1.827

Review 3.  Adjuvant therapy in biliary atresia: hopelessly optimistic or potential for change?

Authors:  Mark Davenport
Journal:  Pediatr Surg Int       Date:  2017-09-22       Impact factor: 1.827

Review 4.  Biliary atresia: unity in diversity.

Authors:  Claus Petersen
Journal:  Pediatr Surg Int       Date:  2017-10-05       Impact factor: 1.827

Review 5.  Surgical modifications, additions, and alternatives to Kasai hepato-portoenterostomy to improve the outcome in biliary atresia.

Authors:  Shilpa Sharma; Devendra K Gupta
Journal:  Pediatr Surg Int       Date:  2017-10-04       Impact factor: 1.827

Review 6.  Recent advances in the pathogenesis and management of biliary atresia.

Authors:  Jessica A Zagory; Marie V Nguyen; Kasper S Wang
Journal:  Curr Opin Pediatr       Date:  2015-06       Impact factor: 2.856

7.  Use of corticosteroids after hepatoportoenterostomy for bile drainage in infants with biliary atresia: the START randomized clinical trial.

Authors:  Jorge A Bezerra; Cathie Spino; John C Magee; Benjamin L Shneider; Philip Rosenthal; Kasper S Wang; Jessi Erlichman; Barbara Haber; Paula M Hertel; Saul J Karpen; Nanda Kerkar; Kathleen M Loomes; Jean P Molleston; Karen F Murray; Rene Romero; Kathleen B Schwarz; Ross Shepherd; Frederick J Suchy; Yumirle P Turmelle; Peter F Whitington; Jeffrey Moore; Averell H Sherker; Patricia R Robuck; Ronald J Sokol
Journal:  JAMA       Date:  2014-05-07       Impact factor: 56.272

8.  Efficacy of and prognosis after steroid pulse therapy in patients with poor reduction of jaundice after laparoscopic Kasai portoenterostomy.

Authors:  Yujiro Tanaka; Chiyoe Shirota; Takahisa Tainaka; Wataru Sumida; Kazuo Oshima; Satoshi Makita; Tomoko Tanaka; Yukiko Tani; Kosuke Chiba; Hiroo Uchida
Journal:  Pediatr Surg Int       Date:  2019-08-08       Impact factor: 1.827

Review 9.  Adjuvant steroid treatment following Kasai portoenterostomy and clinical outcomes of biliary atresia patients: an updated meta-analysis.

Authors:  Min-Zhong Zhang; Peng-Cheng Xun; Ka He; Wei Cai
Journal:  World J Pediatr       Date:  2016-10-15       Impact factor: 2.764

Review 10.  Beyond the Pediatric end-stage liver disease system: solutions for infants with biliary atresia requiring liver transplant.

Authors:  Mary Elizabeth M Tessier; Sanjiv Harpavat; Ross W Shepherd; Girish S Hiremath; Mary L Brandt; Amy Fisher; John A Goss
Journal:  World J Gastroenterol       Date:  2014-08-28       Impact factor: 5.742

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