Congenital intrapericardial diaphragmatic hernia with omphalocele.

Congenital intrapericardial diaphragmatic hernia with omphalocele is very rare. Few cases have been reported in the literature. The embryologic mechanism of this is considered to be abnormal development of the ventral mesoderm at 3-4 weeks after conception. Sometimes, omphalocele is repaired, rather than intrapericardial diaphragmatic hernia, thus causing serious consequences because of the high intra-abdominal pressure. In this paper, we present a case who underwent successful open repair.