| Literature DB >> 23639747 |
Wei Xu1, Hui Wu2, Dong-Xuan Wang3, Zhi-Hong Mu1.
Abstract
Prune belly syndrome (PBS) is a rare congenital disorder characterized by deficient abdominal wall muscles, urinary tract malformation, and, in males, cryptorchidism. We present a case of PBS in China. The patient was a newborn baby boy who had wrinkled, "prune-like" abdominal skin, bilateral cryptorchidism, and urinary system malformation, complicated with hypoplasia of the lung and branch of the coronary artery-right ventricular fistula. His kidney function was inadequate. The patient subsequently died at age 28 days due to septicemia from a severe urinary tract infection.Entities:
Keywords: abdominal wall musculature deficiency; bilateral cryptorchidism; prune belly syndrome; urinary tract anomalies
Mesh:
Year: 2013 PMID: 23639747 DOI: 10.1016/j.pedneo.2013.03.014
Source DB: PubMed Journal: Pediatr Neonatol ISSN: 1875-9572 Impact factor: 2.083