Literature DB >> 23639747

A case of prune belly syndrome.

Wei Xu1, Hui Wu2, Dong-Xuan Wang3, Zhi-Hong Mu1.   

Abstract

Prune belly syndrome (PBS) is a rare congenital disorder characterized by deficient abdominal wall muscles, urinary tract malformation, and, in males, cryptorchidism. We present a case of PBS in China. The patient was a newborn baby boy who had wrinkled, "prune-like" abdominal skin, bilateral cryptorchidism, and urinary system malformation, complicated with hypoplasia of the lung and branch of the coronary artery-right ventricular fistula. His kidney function was inadequate. The patient subsequently died at age 28 days due to septicemia from a severe urinary tract infection.
Copyright © 2013. Published by Elsevier B.V.

Entities:  

Keywords:  abdominal wall musculature deficiency; bilateral cryptorchidism; prune belly syndrome; urinary tract anomalies

Mesh:

Year:  2013        PMID: 23639747     DOI: 10.1016/j.pedneo.2013.03.014

Source DB:  PubMed          Journal:  Pediatr Neonatol        ISSN: 1875-9572            Impact factor:   2.083


  2 in total

1.  Prune-belly syndrome: an autopsy case report.

Authors:  Marcela Arruda Pereira Silva Vasconcelos; Patricia Picciarelli de Lima
Journal:  Autops Case Rep       Date:  2014-03-30

2.  Prune-Belly syndrome, a rare case presentation in neonatology: about one case in Yaounde, Cameroon.

Authors:  Dany Hermann Ngwanou; Emmanuel Ngantchet; Georges Pius Kamsu Moyo
Journal:  Pan Afr Med J       Date:  2020-06-17
  2 in total

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