Literature DB >> 23636243

Compromised shear-dependent cleavage of type 2N von Willebrand factor variants by ADAMTS13 in the presence of factor VIII.

Christopher G Skipwith, Sandra L Haberichter, Ashley Gehrand, X Long Zheng.   

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Year:  2013        PMID： 23636243      PMCID： PMC3813456          DOI： 10.1160/TH13-01-0053

Source DB:  PubMed          Journal:  Thromb Haemost        ISSN： 0340-6245            Impact factor:   5.249


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  14 in total

1.  Two novel type 2N von Willebrand disease-causing mutations that result in defective factor VIII binding, multimerization, and secretion of von Willebrand factor.

Authors:  S Allen; A M Abuzenadah; J L Blagg; J Hinks; I M Nesbitt; A C Goodeve; T Gursel; J Ingerslev; I R Peake; M E Daly
Journal:  Blood       Date:  2000-03-15       Impact factor: 22.113

2.  Exosite interactions contribute to tension-induced cleavage of von Willebrand factor by the antithrombotic ADAMTS13 metalloprotease.

Authors:  Weiqiang Gao; Patricia J Anderson; Elaine M Majerus; Elodee A Tuley; J Evan Sadler
Journal:  Proc Natl Acad Sci U S A       Date:  2006-12-04       Impact factor: 11.205

Review 3.  The genetic basis of von Willebrand disease.

Authors:  Anne C Goodeve
Journal:  Blood Rev       Date:  2010-04-20       Impact factor: 8.250

4.  von Willebrand factor-cleaving protease in thrombotic thrombocytopenic purpura and the hemolytic-uremic syndrome.

Authors:  M Furlan; R Robles; M Galbusera; G Remuzzi; P A Kyrle; B Brenner; M Krause; I Scharrer; V Aumann; U Mittler; M Solenthaler; B Lämmle
Journal:  N Engl J Med       Date:  1998-11-26       Impact factor: 91.245

5.  Factor VIII accelerates proteolytic cleavage of von Willebrand factor by ADAMTS13.

Authors:  Wenjing Cao; Sriram Krishnaswamy; Rodney M Camire; Peter J Lenting; X Long Zheng
Journal:  Proc Natl Acad Sci U S A       Date:  2008-05-20       Impact factor: 11.205

6.  Abnormal binding of factor VIII is linked with the substitution of glutamine for arginine 91 in von Willebrand factor in a variant form of von Willebrand disease.

Authors:  P A Kroner; K D Friedman; S A Fahs; J P Scott; R R Montgomery
Journal:  J Biol Chem       Date:  1991-10-15       Impact factor: 5.157

7.  The defective interaction between von Willebrand factor and factor VIII in a patient with type 1 von Willebrand disease is caused by substitution of Arg19 and His54 in mature von Willebrand factor.

Authors:  P A Kroner; P A Foster; S A Fahs; R R Montgomery
Journal:  Blood       Date:  1996-02-01       Impact factor: 22.113

8.  An Arg760Cys mutation in the consensus sequence of the von Willebrand factor propeptide cleavage site is responsible for a new von Willebrand disease variant.

Authors:  Alessandra Casonato; Francesca Sartorello; Maria Grazia Cattini; Elena Pontara; Carmen Soldera; Antonella Bertomoro; Antonio Girolami
Journal:  Blood       Date:  2002-08-08       Impact factor: 22.113

9.  Recombinant expression of mutations causing von Willebrand disease type Normandy: characterization of a combined defect of factor VIII binding and multimerization.

Authors:  Reinhard Schneppenheim; Harald Lenk; Tobias Obser; Johannes Oldenburg; Florian Oyen; Sonja Schneppenheim; Rainer Schwaab; Kerstin Will; Ulrich Budde
Journal:  Thromb Haemost       Date:  2004-07       Impact factor: 5.249

10.  Light chain of factor VIII is sufficient for accelerating cleavage of von Willebrand factor by ADAMTS13 metalloprotease.

Authors:  Wenjing Cao; Denise E Sabatino; Ekaterina Altynova; Amy M Lange; Veronica C Casina; Rodney M Camire; X Long Zheng
Journal:  J Biol Chem       Date:  2012-08-01       Impact factor: 5.157
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  1 in total

1.  Factor VIII binding affects the mechanical unraveling of the A2 domain of von Willebrand factor.

Authors:  Wenpeng Cao; Wenjing Cao; Wei Zhang; X Long Zheng; X Frank Zhang
Journal:  J Thromb Haemost       Date:  2020-07-23       Impact factor: 5.824
  1 in total

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