Petr Santavy1. 1. Department of Cardiac Surgery, University Hospital Olomouc, Czech Republic. petr.santavy@fnol.cz
Abstract
BACKGROUND: Marfan syndrome (MFS) is the most common inherited disorder of connective tissue affecting multiple organ systems. The most life-threatening and life-shortening complication is aortic dissection. Without surgery, life expectancy of MFS patients is reduced to approximately 32 years. Early identification and appropriate multidisciplinary medical cooperation is essential. CONCLUSION: Proper follow up, therapy and timely surgical repair lead to an almost normal lifespan in affected individuals.
BACKGROUND:Marfan syndrome (MFS) is the most common inherited disorder of connective tissue affecting multiple organ systems. The most life-threatening and life-shortening complication is aortic dissection. Without surgery, life expectancy of MFSpatients is reduced to approximately 32 years. Early identification and appropriate multidisciplinary medical cooperation is essential. CONCLUSION: Proper follow up, therapy and timely surgical repair lead to an almost normal lifespan in affected individuals.
Authors: María Luisa Gutiérrez García; Sara Blasco-Algora; Conrado M Fernández-Rodríguez Journal: World J Gastroenterol Date: 2015-07-28 Impact factor: 5.742